Hereditary Sensory and Motor Neuropathy (Dejerine Sottas Disease)

A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include HMSNs I-VII. HMSN I and II both refer to CHARCOT-MARIE-TOOTH DISEASE. HMSN III refers to hypertrophic neuropathy of infancy. HMSN IV refers to REFSUM DISEASE. HMSN V refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia (see SPASTIC PARAPLEGIA, HEREDITARY). HMSN VI refers to HMSN associated with an inherited optic atrophy (OPTIC ATROPHIES, HEREDITARY), and HMSN VII refers to HMSN associated with retinitis pigmentosa. (From Adams et al., Principles of Neurology, 6th ed, p1343)
Also Known As:
Dejerine Sottas Disease; HMSN; Herditary Sensory and Motor Neuropathy; Hereditary Motor and Sensory Neuropathy; Disease, Dejerine-Sottas; HMSN Type IIIs; HMSN Type VIIs; Type VII, HMSN; Dejerine-Sottas Disease; HMSN Type III; HMSN Type VII; Hereditary Motor and Sensory Neuropathies; Hereditary, Type III, Motor and Sensory Neuropathy; Hereditary, Type VII, Motor and Sensory Neuropathy; Neuropathies, Hereditary Motor and Sensory
Networked: 149 relevant articles (1 outcomes, 14 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hereditary Sensory and Motor Neuropathy (Dejerine Sottas Disease)
2. Charcot-Marie-Tooth Disease (Peroneal Muscular Atrophy)
3. Spinal Muscular Atrophy (Progressive Muscular Atrophy)
4. Neoplasms (Cancer)
5. Cataract (Cataracts)


1. Thomas, P K: 6 articles (08/2003 - 05/2000)
2. Shekarabi, Masoud: 5 articles (01/2013 - 09/2008)
3. Laganière, Janet: 5 articles (01/2013 - 09/2008)
4. Rouleau, Guy A: 5 articles (01/2013 - 09/2008)
5. Salin-Cantegrel, Adèle: 4 articles (01/2013 - 09/2008)
6. Kalaydjieva, L: 4 articles (12/2000 - 07/2000)
7. King, R H: 4 articles (12/2000 - 05/2000)
8. Angelicheva, D: 4 articles (12/2000 - 07/2000)
9. Dion, Patrick A: 3 articles (01/2013 - 08/2011)
10. Rasheed, Sarah: 3 articles (01/2013 - 08/2011)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hereditary Sensory and Motor Neuropathy:
1. Retinaldehyde (Retinal)IBA
2. LOM type hereditary motor and sensory NeuropathyIBA
3. Myelin P0 Protein (Myelin Protein Zero)IBA
4. DNA (Deoxyribonucleic Acid)IBA
5. Silicon Dioxide (Sand)FDA LinkGeneric
6. Myelin ProteinsIBA
7. BrachyolmiaIBA
8. Russe type hereditary motor and sensory NeuropathyIBA
9. Type 2C Charcot-Marie-Tooth diseaseIBA
10. Lipid AIBA

Therapies and Procedures

1. Denervation
2. Resistance Training
3. X-Ray Film
4. Individualized Medicine
5. Cochlear Implantation