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Uroporphyrinogen Decarboxylase (Uroporphyrinogen III Decarboxylase)

An enzyme that catalyzes the decarboxylation of UROPORPHYRINOGEN III to coproporphyrinogen III by the conversion of four acetate groups to four methyl groups. It is the fifth enzyme in the 8-enzyme biosynthetic pathway of HEME. Several forms of cutaneous PORPHYRIAS are results of this enzyme deficiency as in PORPHYRIA CUTANEA TARDA; and HEPATOERYTHROPOIETIC PORPHYRIA.
Also Known As:
Uroporphyrinogen III Decarboxylase; Carboxy-Lyase, Uroporphyrinogen; Decarboxylase, Uroporphyrinogen; Decarboxylase, Uroporphyrinogen III; Uroporphyrinogen Carboxy Lyase; Uroporphyrinogen Carboxy-Lyase; Uroporphyrinogen-III carboxy-lyase
Networked: 247 relevant articles (2 outcomes, 14 trials/studies)

Relationship Network

Bio-Agent Context: Research Results

Experts

1. Anderson, Karl E: 5 articles (11/2019 - 02/2002)
2. Phillips, John D: 5 articles (11/2019 - 10/2002)
3. Phillips, J D: 5 articles (09/2011 - 01/2001)
4. Desnick, Robert J: 4 articles (11/2019 - 05/2010)
5. Méndez, Manuel: 4 articles (06/2013 - 02/2004)
6. Kushner, James P: 4 articles (12/2011 - 10/2002)
7. Sandberg, Sverre: 3 articles (01/2022 - 04/2009)
8. To-Figueras, Jordi: 3 articles (11/2019 - 11/2010)
9. Morán-Jiménez, María-Josefa: 3 articles (06/2013 - 08/2010)
10. Grady, James J: 3 articles (12/2012 - 03/2010)

Related Diseases

1. Porphyria Cutanea Tarda
2. Hepatoerythropoietic Porphyria
3. Porphyrias (Porphyria)
4. Hepatic Porphyrias (Hepatic Porphyria)
5. Hemochromatosis (Bronze Diabetes)

Related Drugs and Biologics

1. Iron
2. Enzymes
3. DNA (Deoxyribonucleic Acid)
4. Hexachlorobenzene (HCB)
5. Polychlorinated Dibenzodioxins (TCDD)
6. Mixed Function Oxygenases (Monooxygenases)
7. Hydrocarbons
8. Cytochrome P-450 CYP1A1 (CYP1A1)
9. Liver Extracts
10. Genetic Markers (Genetic Marker)

Related Therapies and Procedures

1. Radiotherapy
2. Renal Dialysis (Hemodialysis)