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Essential Thrombocythemia

A clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.
Also Known As:
Thrombocythemia, Essential; Primary Thrombocythemia; Thrombocytosis, Autosomal Dominant; Thrombocytosis, Primary; Autosomal Dominant Thrombocytoses; Autosomal Dominant Thrombocytosis; Dominant Thrombocytoses, Autosomal; Dominant Thrombocytosis, Autosomal; Essential Thrombocythemias; Hemorrhagic Thrombocythemias; Idiopathic Thrombocythemia; Idiopathic Thrombocythemias; Primary Thrombocythemias; Primary Thrombocytoses; Primary Thrombocytosis; Thrombocythemias, Essential; Thrombocythemias, Hemorrhagic; Thrombocythemias, Idiopathic; Thrombocythemias, Primary; Thrombocytoses, Autosomal Dominant; Thrombocytoses, Primary; Hemorrhagic Thrombocythemia; Thrombocythemia, Hemorrhagic; Thrombocythemia, Idiopathic; Thrombocythemia, Primary
Networked: 1298 relevant articles (60 outcomes, 131 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Polycythemia Vera
2. Thrombosis (Thrombus)
3. Primary Myelofibrosis (Myelosclerosis)
4. Myeloproliferative Disorders (Myeloproliferative Disorder)
5. Thrombocytosis (Thrombocythemia)

Experts

1. Vannucchi, Alessandro M: 39 articles (12/2022 - 09/2005)
2. Tefferi, Ayalew: 38 articles (01/2019 - 01/2004)
3. Verstovsek, Srdan: 31 articles (11/2021 - 01/2003)
4. Barbui, Tiziano: 29 articles (12/2022 - 05/2003)
5. Guglielmelli, Paola: 24 articles (01/2021 - 09/2005)
6. Mesa, Ruben A: 21 articles (12/2022 - 04/2005)
7. Rambaldi, Alessandro: 20 articles (12/2022 - 08/2010)
8. Finazzi, Guido: 18 articles (01/2019 - 05/2003)
9. Constantinescu, Stefan N: 17 articles (07/2021 - 12/2005)
10. Passamonti, Francesco: 15 articles (12/2021 - 09/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Essential Thrombocythemia:
1. Hydroxyurea (Hydrea)FDA LinkGeneric
2. Aspirin (Acetylsalicylic Acid)FDA LinkGeneric
3. anagrelide (Agrylin)FDA LinkGeneric
4. Interferon-alpha (Interferon Alfa)IBA
5. InterferonsIBA
6. Busulfan (Busulfex)FDA Link
7. ranimustineIBA
8. ruxolitinibIBA
9. Janus Kinase 2IBA
10. Hemoglobins (Hemoglobin)IBA

Therapies and Procedures

1. Therapeutics
2. Aftercare (After-Treatment)
3. Splenectomy
4. Combination Drug Therapy (Combination Chemotherapy)
5. Bloodletting