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Retroperitoneal Fibrosis

A slowly progressive condition of unknown etiology, characterized by deposition of fibrous tissue in the retroperitoneal space compressing the ureters, great vessels, bile duct, and other structures. When associated with abdominal aortic aneurysm, it may be called chronic periaortitis or inflammatory perianeurysmal fibrosis.
Also Known As:
Fibrosis, Inflammatory Perianeurysmal; Fibrosis, Perianeurysmal Inflammatory; Idiopathic Retroperitoneal Fibrosis; Inflammatory Fibrosis, Perianeurysmal; Inflammatory Perianeurysmal Fibrosis; Ormond's Disease; Perianeurysmal Inflammatory Fibrosis; Chronic Periaortitides; Chronic Periaortitis; Disease, Ormond; Disease, Ormond's; Fibroses, Retroperitoneal; Fibrosis, Retroperitoneal; Periaortitides, Chronic; Retroperitoneal Fibroses; Ormond Disease; Perianeurysmal Fibrosis, Inflammatory; Periaortitis, Chronic
Networked: 715 relevant articles (44 outcomes, 25 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Neoplasms (Cancer)
2. Immunoglobulin G4-Related Disease
3. Aggressive Fibromatosis (Desmoid)
4. Lymphoma (Lymphomas)
5. Membranous Glomerulonephritis (Membranous Nephropathy)

Experts

1. Vaglio, Augusto: 18 articles (10/2021 - 01/2005)
2. Salvarani, Carlo: 10 articles (03/2017 - 01/2006)
3. Buzio, Carlo: 10 articles (08/2014 - 01/2005)
4. Maritati, Federica: 9 articles (10/2021 - 06/2011)
5. Palmisano, Alessandra: 8 articles (01/2020 - 06/2011)
6. Kamisawa, Terumi: 8 articles (12/2015 - 05/2005)
7. Okazaki, Kazuichi: 7 articles (01/2019 - 12/2005)
8. van Bommel, E F H: 6 articles (10/2022 - 07/2002)
9. Pipitone, Nicolò: 6 articles (01/2019 - 01/2011)
10. Uchida, Kazushige: 6 articles (10/2015 - 12/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Retroperitoneal Fibrosis:
1. TamoxifenFDA LinkGeneric
2. SteroidsIBA
3. Adrenal Cortex Hormones (Corticosteroids)IBA
4. Mycophenolic Acid (Cellcept)FDA LinkGeneric
5. GlucocorticoidsIBA
6. Prednisone (Sone)FDA LinkGeneric
7. Pergolide (Permax)FDA Link
8. Prednisolone (Predate)FDA LinkGeneric
9. Rituximab (Mabthera)FDA Link
10. Cyclophosphamide (Cytoxan)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Radiotherapy
3. Operative Surgical Procedures
4. Aftercare (After-Treatment)
5. Drug Therapy (Chemotherapy)