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Pseudohypoparathyroidism

A hereditary syndrome clinically similar to HYPOPARATHYROIDISM. It is characterized by HYPOCALCEMIA; HYPERPHOSPHATEMIA; and associated skeletal development impairment and caused by failure of response to PARATHYROID HORMONE rather than deficiencies. A severe form with resistance to multiple hormones is referred to as Type 1a and is associated with maternal mutant allele of the ALPHA CHAIN OF STIMULATORY G PROTEIN.
Also Known As:
Albright Hereditary Osteodystrophy with Multiple Hormone Resistance; PHD Ib; PHD1b; PHP Ia; Pseudohypoparathyroidism Type 1B; Pseudohypoparathyroidism, Type Ia; Pseudohypoparathyroidism, Type Ib; Hereditary Osteodystrophy, Albright; Osteodystrophy, Albright Hereditary; Pseudohypoparathyroidism Type 1Bs; Pseudohypoparathyroidisms; Pseudohypoparathyroidisms, Type Ia; Pseudohypoparathyroidisms, Type Ib; Type Ia Pseudohypoparathyroidism; Type Ia Pseudohypoparathyroidisms; Type Ib Pseudohypoparathyroidism; Type Ib Pseudohypoparathyroidisms; Albright Hereditary Osteodystrophy; PHPIa
Networked: 756 relevant articles (7 outcomes, 30 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hypoparathyroidism
2. Secondary Parkinson Disease (Secondary Parkinsonism)
3. Pseudohypoparathyroidism
4. Hypocalcemia
5. Primary Hyperparathyroidism

Experts

1. Jüppner, Harald: 36 articles (06/2022 - 09/2003)
2. Mantovani, Giovanna: 31 articles (01/2022 - 09/2003)
3. Linglart, Agnès: 23 articles (01/2022 - 01/2002)
4. Bastepe, Murat: 23 articles (01/2020 - 09/2003)
5. Reyes, Monica: 14 articles (01/2022 - 04/2012)
6. de Sanctis, Luisa: 14 articles (02/2021 - 04/2004)
7. Hiort, Olaf: 13 articles (01/2020 - 04/2003)
8. Levine, Michael A: 13 articles (01/2020 - 08/2002)
9. Thiele, Susanne: 13 articles (01/2020 - 09/2008)
10. Spada, Anna: 13 articles (01/2018 - 09/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Pseudohypoparathyroidism:
1. CalciumIBA
2. Parathyroid Hormone (Parathormone)IBA
3. Vitamin DFDA LinkGeneric
4. Thyrotropin (Thyroid-Stimulating Hormone)FDA Link
5. Growth Hormone (Somatotropin)IBA
6. GonadotropinsIBA
7. 1,25-dihydroxyvitamin DIBA
8. 5-phenylpent-4-enyl-1-hydroperoxideIBA
9. Hormones (Hormone)IBA
10. Proteins (Proteins, Gene)FDA Link

Therapies and Procedures

1. Therapeutics
2. Aftercare (After-Treatment)
3. Oral Administration
4. Parathyroidectomy
5. Ligation