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Pseudohypoaldosteronism

A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.
Also Known As:
Familial Hyperpotassemia and Hypertension; Familial Hypertensive Hyperkalemia; Pseudohypoaldosteronism Type 1, Autosomal Dominant; Pseudohypoaldosteronism Type 2; Pseudohypoaldosteronism Type I; Pseudohypoaldosteronism Type II; Familial Hypertensive Hyperkalemias; Gordon Hyperkalemia Hypertension Syndrome; Hyperkalemia, Familial Hypertensive; Hyperkalemia-Hypertension Syndrome, Gordon; Hyperkalemias, Familial Hypertensive; Hypertensive Hyperkalemias, Familial; Pseudohypoaldosteronism Type 1s; Pseudohypoaldosteronism Type 2s; Pseudohypoaldosteronism Type IIs; Pseudohypoaldosteronism Type Is; Pseudohypoaldosteronisms; Pseudohypoaldosteronisms, Type I; Pseudohypoaldosteronisms, Type II; Syndrome, Gordon Hyperkalemia-Hypertension; Type 1, Pseudohypoaldosteronism; Type I Pseudohypoaldosteronism; Type I, Pseudohypoaldosteronism; Type II Pseudohypoaldosteronism; Type II Pseudohypoaldosteronisms; Type II, Pseudohypoaldosteronism; Type IIs, Pseudohypoaldosteronism; Type Is, Pseudohypoaldosteronism; Gordon Hyperkalemia-Hypertension Syndrome; Hyperpotassemia and Hypertension, Familial; Hypertensive Hyperkalemia, Familial; Pseudohypoaldosteronism Type 1; Pseudohypoaldosteronism Type 1, Autosomal Recessive; Pseudohypoaldosteronism, Type I; Pseudohypoaldosteronism, Type I, Autosomal Dominant; Pseudohypoaldosteronism, Type I, Autosomal Recessive; Pseudohypoaldosteronism, Type II
Networked: 475 relevant articles (2 outcomes, 19 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hypertension (High Blood Pressure)
2. Liddle Syndrome
3. Glucocorticoid-Remediable Aldosteronism
4. Apparent Mineralocorticoid Excess Syndrome
5. Hypotension (Low Blood Pressure)

Experts

1. Uchida, Shinichi: 34 articles (11/2020 - 12/2005)
2. Sohara, Eisei: 24 articles (01/2020 - 10/2009)
3. Rai, Tatemitsu: 24 articles (12/2018 - 10/2006)
4. Sasaki, Sei: 19 articles (11/2015 - 10/2006)
5. Mori, Takayasu: 15 articles (11/2020 - 03/2013)
6. Chiga, Motoko: 14 articles (11/2020 - 10/2006)
7. Lifton, Richard P: 14 articles (01/2018 - 01/2003)
8. Gamba, Gerardo: 13 articles (01/2022 - 01/2003)
9. Zennaro, Maria-Christina: 13 articles (11/2020 - 06/2003)
10. Riepe, Felix G: 13 articles (05/2013 - 04/2003)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Pseudohypoaldosteronism:
1. SaltsIBA
2. AldosteroneIBA
3. ReninIBA
4. Epithelial Sodium ChannelsIBA
5. MineralocorticoidsIBA
6. Lysine (L-Lysine)FDA Link
7. Hydrocortisone (Cortisol)FDA LinkGeneric
8. Complementary DNA (cDNA)IBA
9. Mineralocorticoid Receptors (Mineralocorticoid Receptor)IBA
10. Phosphotransferases (Kinase)IBA

Therapies and Procedures

1. Therapeutics
2. Fluid Therapy (Oral Rehydration Therapy)
3. Ileostomy
4. Precision Medicine
5. Kidney Transplantation