Prune Belly Syndrome

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76 relevant articles (2 outcomes, 2 trials/studies) found for this Disease

Description: A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin.

Also Known As:

Prune-Belly Syndrome; Belly Syndrome, Prune; Belly Syndromes, Prune; Prune Belly Syndromes; Prune-Belly Syndromes; Syndrome, Prune Belly; Syndrome, Prune-Belly; Syndromes, Prune Belly; Syndromes, Prune-Belly

Relationship Network

Disease Context: Research Results

Congenital, Hereditary, and Neonatal Diseases and Abnormalities: 422

Congenital Abnormalities: 9332

Multiple Abnormalities: 120

Prune Belly Syndrome: 76

Related Diseases

1.	Kidney Failure (Renal Failure)
2.	Cryptorchidism (Undescended Testes)
3.	Syndrome
4.	Neurogenic Urinary Bladder (Bladder, Neurogenic)
5.	Chronic Kidney Failure (Chronic Renal Failure)

Experts

1.	Edghill, Emma L: 1 article (07/2008)
2.	Thomas, Katie: 1 article (07/2008)
3.	Murray, Paul J: 1 article (07/2008)
4.	Bingham, Coralie: 1 article (07/2008)
5.	Mulgrew, Christopher J: 1 article (07/2008)
6.	Ellard, Sian: 1 article (07/2008)
7.	Kamel, Mohamed H: 1 article (04/2007)
8.	O'Kelly, Patrick: 1 article (04/2007)
9.	Thomas, Anil A: 1 article (04/2007)
10.	Hickey, David P: 1 article (04/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Prune Belly Syndrome:

1.	Pentetic Acid (DTPA)FDA LinkGeneric 02/01/1986 - "An 18-year-old man with prune belly syndrome had negative renal outlines during a Tc-99m DTPA study" Order ALL the reference details at left...
2.	Triad FDA Link 08/01/2004 - "In addition, the neonate also had triad of signs and symptoms associated with prune belly syndrome" 03/01/1991 - "Prune belly syndrome in females: a triad of abdominal musculature deficiency and anomalies of the urinary and genital systems." 04/01/1989 - "Usually, a triad of congenital anomalies highlights the components of the prune-belly syndrome" 12/01/1976 - "Dilation of the penile urethra is described in a male infant with the classic triad of the prune belly syndrome" 04/01/2008 - "BACKGROUND: Pseudo prune belly syndrome is an incomplete expression of the triad syndrome" Order ALL the reference details at left...
3.	Dihydrotachysterol (AT 10)IBA 11/01/1998 - "We present a case of prune belly syndrome in a 12-week fetus whose previous anomaly scan at 10 weeks had been normal" 09/01/1997 - "RESULTS: Graft survival in the prune-belly syndrome and control groups was 50 and 72% at 5 years, and 50 and 47% at 10 years, respectively (not statistically significant)" 09/01/1997 - "No statistically significant increase in serum creatinine was noted at 10 years in children with the prune-belly syndrome" Order ALL the reference details at left...
4.	CreatinineIBA 01/01/2000 - "One of the patients with prune belly syndrome was 18 months old at last follow-up, with hydrocephalus and a creatinine level of 0.2 mg/dL" 09/01/1997 - "No statistically significant increase in serum creatinine was noted at 10 years in children with the prune-belly syndrome" Order ALL the reference details at left...
5.	Hepatocyte Nuclear Factor 1-betaIBA 07/01/2008 - "Whole gene deletion of the hepatocyte nuclear factor-1beta gene in a patient with the prune-belly syndrome." Order ALL the reference details at left...
6.	alpha-1 Adrenergic Receptors (alpha 1 Adrenergic Receptor)IBA 09/01/1999 - "MATERIALS AND METHODS: We treated 17 children 3 to 15 years old with documented poor bladder emptying of various etiologies, including dysfunctional voiding, the Hinman syndrome, the lazy bladder syndrome, posterior urethral valves, myelomeningocele and the prune-belly syndrome, using the alpha-1 adrenergic receptor antagonist, doxazosin" Order ALL the reference details at left...
7.	Doxazosin (Cardura)FDA LinkGeneric 09/01/1999 - "MATERIALS AND METHODS: We treated 17 children 3 to 15 years old with documented poor bladder emptying of various etiologies, including dysfunctional voiding, the Hinman syndrome, the lazy bladder syndrome, posterior urethral valves, myelomeningocele and the prune-belly syndrome, using the alpha-1 adrenergic receptor antagonist, doxazosin" Order ALL the reference details at left...
8.	UreaseIBA 10/01/1998 - "Although particularly associated with Proteus infections and prune belly syndrome, hyperammonaemia can complicate infection with any urease-producing bacteria if there is urinary stasis." Order ALL the reference details at left...
9.	Polypropylenes (Polypropylene)IBA 10/01/1993 - "In 1 patient the testis was involved in Marlex mesh, 1 had had two prior orchidopexies, and 1 had prune belly syndrome" Order ALL the reference details at left...
10.	ElectrolytesIBA 08/01/1990 - "In 2 cases with oligohydramnios fetal urinary electrolytes were suggestive of satisfactory renal function but the infants died of pulmonary hypoplasia and had bilateral renal dysplasia, prune belly syndrome and urethral atresia" Order ALL the reference details at left...

Therapies and Procedures

1.	Kidney Transplantation 09/01/1997 - "PURPOSE: We assessed the long-term efficacy of renal transplantation in children with the prune-belly syndrome" 04/01/2007 - "OBJECTIVES: To present the long-term outcome of deceased-donor kidney transplantation in prune belly syndrome (PBS)" 04/01/2007 - "Deceased-donor kidney transplantation in prune belly syndrome." 10/01/2004 - "We assess the effect of the prune-belly syndrome (PBS) on renal transplantation outcome" 10/01/2004 - "Renal transplantation in prune-belly syndrome." Order ALL the reference details at left...
2.	Decompression 05/01/2000 - "Histology of the fetal prune belly syndrome with reference to the efficacy of prenatal decompression." 06/01/2003 - "Even though most children with Prune Belly Syndrome respond to lower urinary tract drainage, a cutaneous pyelostomy may be necessary when the ureters are tortuous and do not drain adequately following bladder decompression." 07/01/1993 - "Development of the Eagle-Barrett (prune belly) syndrome and a thickened, poorly functional bladder wall after early second-trimester decompression of fetal megacystis." Order ALL the reference details at left...
3.	Transplants (Transplant) 09/01/2005 - "Posterior urethral valves were confirmed in 7 males, urethral atresia in 4, and prune belly syndrome in 7. Eight children had acceptable renal function, 4 had mild insufficiency, and 6 required dialysis and eventual renal transplant" 12/01/1989 - "There was no statistically significant difference in patient deaths (1 versus 3), graft survival (75 versus 69%) or graft function between patients with the prune belly syndrome and controls" 09/01/2003 - "Torsion of a renal transplant around its pedicle is a rare complication, which has been described in renal transplant children with Prune Belly syndrome, but also exceptionally in adults undergoing kidney-pancreas transplantation" 02/01/1995 - "We report a 26-month-old child diagnosed with prune-belly syndrome and end-stage renal disease who received intraperitoneal implantation of an adult cadaveric renal graft which functioned very well for approximately 6 weeks" 01/01/1989 - "This is a case history of a prune-belly syndrome with multiple urologic disorders leading to a renal transplant due to a chronic renal failure at age 8. After four allograft pyelolithotomies he was referred to us with a staghorn stone in the same graft" Order ALL the reference details at left...
4.	Peritoneal Dialysis 01/01/1994 - "OBJECTIVES: To describe our experience with chronic ambulatory peritoneal dialysis in children with the prune belly syndrome (PBS)" 01/01/1994 - "Peritoneal dialysis in the prune belly syndrome." 12/01/2006 - "We describe a 7-year-old African-American boy with prune-belly syndrome who developed acute onset of peritoneal eosinophilia after placement of a peritoneal dialysis catheter" 12/01/2006 - "Acute peritoneal eosinophilia in a child with prune-belly syndrome following peritoneal dialysis catheter placement." 09/01/1999 - "Bowel perforation due to hypotension in an infant with prune belly syndrome undergoing peritoneal dialysis." Order ALL the reference details at left...
5.	Transplantation (Transplant Recipients) 09/01/1997 - "Two patients with the prune-belly syndrome underwent internal urethrotomy after transplantation" 12/01/1989 - "Patients with the prune belly syndrome waited a shorter interval for transplantation than did controls (no statistically significant difference) because the distensible abdominal wall characteristic of the syndrome permits placement of an adult kidney in a young child" 12/01/1989 - "The effect of the prune belly syndrome on the outcome of renal transplantation was evaluated in a retrospective study in which 8 transplant recipients with this syndrome were randomly matched with 13 control, nondiabetic transplant patients" 11/01/2004 - "The cause of urinary tract disorders included: meningomyelocele connected with neuropathic bladder (n = 4 transplantations); prune belly syndrome (n = 5 transplantations); VATER association (n = 2 transplantations); posterior urethral valves (n = 27 transplantations); and vesico-uretero-renal reflux (n = 28 transplantations)" Order ALL the reference details at left...

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