An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.
Also Known As:
Phenylalanine 4 Monooxygenase; Phenylalanine 4-Hydroxylase; Phenylalanine 4-Monooxygenase; 4-Hydroxylase, Phenylalanine; 4-Monooxygenase, Phenylalanine; Hydroxylase, Phenylalanine; Phenylalanine 4 Hydroxylase; L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)