A relatively rare, usually benign neoplasm originating in the chemoreceptor tissue of the CAROTID BODY; GLOMUS JUGULARE; GLOMUS TYMPANICUM; AORTIC BODIES; and the female genital tract. It consists histologically of rounded or ovoid hyperchromatic cells that tend to be grouped in an alveolus-like pattern within a scant to moderate amount of fibrous stroma and a few large thin-walled vascular channels. (From Stedman, 27th ed)
Also Known As:
Paraganglioma, Extra Adrenal; Chemodectoma; Paraganglioma, Extra-Adrenal; Chemodectomas; Paraganglioma, Non-Chromaffin; Paragangliomas, Familial Nonchromaffin, 1; Extra-Adrenal Paragangliomas; Non-Chromaffin Paraganglioma; Non-Chromaffin Paragangliomas; Nonchromaffin Paraganglioma; Nonchromaffin Paragangliomas; Paraganglioma, Non Chromaffin; Paragangliomas, Extra-Adrenal; Paragangliomas, Non-Chromaffin; Paragangliomas, Nonchromaffin; Paraganglioma, Nonchromaffin