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Nodular Nonsuppurative Panniculitis (Weber-Christian Disease)

A form of panniculitis characterized by recurrent episodes of fever accompanied by the eruption of single or multiple erythematous subcutaneous nodules on the lower extremities. They normally resolve, but tend to leave depressions in the skin. The condition is most often seen in women, alone or in association with other disorders.
Also Known As:
Weber-Christian Disease; Panniculitis, Nodular Nonsuppurative; Disease, Weber-Christian; Nodular Nonsuppurative Panniculitides; Nonsuppurative Panniculitides, Nodular; Nonsuppurative Panniculitis, Nodular; Panniculitides, Nodular Nonsuppurative; Weber Christian Disease
Networked: 59 relevant articles (8 outcomes, 2 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Panniculitis
2. Psoriasis (Pustulosis Palmaris et Plantaris)
3. Pemphigus (Pemphigus Vulgaris)
4. Bullous Pemphigoid (Pemphigoid)
5. idiopathic Erythema nodosum

Experts

1. Noh, Geunwoong: 2 articles (02/2021 - 01/2021)
2. Egorova, O N: 1 article (06/2021)
3. Kolesnikova, A O: 1 article (06/2021)
4. Musatov, I D: 1 article (06/2021)
5. Radenska-Lopovok, S G: 1 article (06/2021)
6. Severinova, M V: 1 article (06/2021)
7. Han, Chi Wha: 1 article (01/2021)
8. Baikunje, Shashidhar: 1 article (05/2019)
9. Nair, Hari: 1 article (05/2019)
10. Somalanka, Subash: 1 article (05/2019)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Nodular Nonsuppurative Panniculitis:
1. Mycophenolic Acid (Cellcept)FDA LinkGeneric
2. Cyclophosphamide (Cytoxan)FDA LinkGeneric
3. Cyclosporine (Ciclosporin)FDA LinkGeneric
4. Adrenal Cortex Hormones (Corticosteroids)IBA
5. SteroidsIBA
6. Intravenous Immunoglobulins (IVIG)FDA Link
7. Azathioprine (Imuran)FDA LinkGeneric
8. Cytostatic AgentsIBA
9. Adrenocorticotropic Hormone (ACTH)FDA Link
10. Blood Coagulation Factors (Coagulation Factor)IBA

Therapies and Procedures

1. Therapeutics
2. Sclerotherapy
3. Splenectomy
4. Plasma Exchange
5. Jejunoileal Bypass