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Ochronosis

The yellowish discoloration of connective tissue due to deposition of HOMOGENTISIC ACID (a brown-black pigment). This is due to defects in the metabolism of PHENYLALANINE and TYROSINE. Ochronosis occurs in ALKAPTONURIA, but has also been associated with exposure to certain chemicals (e.g., PHENOL, trinitrophenol, BENZENE DERIVATIVES).
Also Known As:
Ochronoses
Networked: 223 relevant articles (2 outcomes, 4 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hyperpigmentation
2. Disease Progression
3. Alkaptonuria
4. Arthritis (Polyarthritis)
5. Joint Diseases (Joint Disease)

Experts

1. Santucci, Annalisa: 14 articles (01/2021 - 10/2010)
2. Gallagher, James A: 13 articles (01/2021 - 11/2010)
3. Ranganath, Lakshminarayan R: 13 articles (01/2021 - 12/2011)
4. Bernardini, Giulia: 10 articles (10/2020 - 10/2010)
5. Braconi, Daniela: 10 articles (01/2020 - 10/2010)
6. Millucci, Lia: 9 articles (01/2021 - 10/2010)
7. Jarvis, Jonathan C: 6 articles (01/2021 - 05/2013)
8. Laschi, Marcella: 6 articles (07/2017 - 10/2010)
9. Spreafico, Adriano: 6 articles (01/2014 - 10/2010)
10. Zatkova, Andrea: 5 articles (01/2022 - 12/2011)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Ochronosis:
1. nitisinone (Orfadin)FDA Link
2. Tretinoin (Retinoic Acid)FDA LinkGeneric
3. SteroidsIBA
4. Homogentisic AcidIBA
5. Tyrosine (L-Tyrosine)FDA Link
6. hydroquinone (Esoterica)FDA Link
7. Melanins (Melanin)IBA
8. Homogentisate 1,2-Dioxygenase (Homogentisate 1,2 Dioxygenase)IBA
9. EnzymesIBA
10. CollagenIBA

Therapies and Procedures

1. Therapeutics
2. Knee Replacement Arthroplasty (Total Knee Replacement)
3. Arthroplasty
4. Replacement Arthroplasty
5. Hip Replacement Arthroplasty (Total Hip Replacement)