An idiopathic syndrome characterized by one or more of the following; recurrent orofacial swelling, relapsing facial paralysis, and fissured tongue (lingua plicata). The onset is usually in childhood and relapses are common. Cheilitis granulomatosa is a monosymptomatic variant of this condition. (Dermatol Clin 1996 Apr;14(2):371-9; Magalini & Magalini, Dictionary of Medical Syndromes, 4th ed, p531)
Also Known As:
Cheilitis Granulomatosa; Cheilitis Granulomatosa, Orofacial Edema, Facial Neuropathy; Facial Neuropathy, Cheilitis Granulomatosa, Orofacial Edema; Facial Neuropathy, Orofacial Edema, Cheilitis Granulomatosa; Macrocheilia, Facial Palsy, Edema; Melkerson-Rosenthal Syndrome; Melkersson Syndrome; Melkersson-Rosenthal-Miescher Syndrome; Miescher-Melkersson-Rosenthal Granulomatous Cheilitis; Orofacial Edema, Cheilitis Granulomatosa, Facial Neuropathy; Orofacial Edema, Facial Neuropathy, Cheilitis Granulomatosa; Rosenthal-Melkerson Syndrome; Rosenthal-Melkersson Syndrome; Syndrome, Melkerson Rosenthal; Cheilitis, Miescher-Melkersson-Rosenthal Granulomatous; Granulomatous Cheilitis, Miescher-Melkersson-Rosenthal; Melkerson Rosenthal Syndrome; Melkersson Rosenthal Miescher Syndrome; Melkersson Rosenthal Syndrome; Miescher Melkersson Rosenthal Granulomatous Cheilitis; Rosenthal Melkerson Syndrome; Rosenthal Melkersson Syndrome; Cheilitis Granulomatosa, Facial Neuropathy, Orofacial Edema; Granulomatous Cheilitis