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Kartagener Syndrome (Kartagener's Syndrome)

An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts.
Also Known As:
Kartagener's Syndrome; Syndrome, Kartagener; Syndrome, Kartagener's; Ciliary Dyskinesia, Primary, 1; Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus; Dextrocardia, Bronchiectasis, and Sinusitis; Kartagener's Triad; Polynesian Bronchiectasis; Siewert Syndrome; Bronchiectasis, Polynesian; Kartageners Syndrome; Kartageners Triad; Polynesian Bronchiectases; Syndrome, Siewert; Kartagener Triad
Networked: 129 relevant articles (2 outcomes, 9 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Chest Pain (Chest Pains)
2. Situs Inversus
3. Cystic Fibrosis (Mucoviscidosis)
4. Usher Syndromes (Usher Syndrome)
5. Retinitis Pigmentosa (Pigmentary Retinopathy)

Experts

1. Buisán, F: 2 articles (11/2021 - 04/2021)
2. Fadrique, A: 2 articles (11/2021 - 04/2021)
3. Ruiz-Bueno, P: 2 articles (11/2021 - 04/2021)
4. Kreisel, Daniel: 2 articles (04/2020 - 01/2019)
5. Kim, Chang Hun: 1 article (02/2022)
6. Kim, Do Hyung: 1 article (02/2022)
7. Son, Bong Soo: 1 article (02/2022)
8. Son, Joohyung: 1 article (02/2022)
9. Dai, Hai-Long: 1 article (01/2022)
10. Du, Yong: 1 article (01/2022)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Kartagener Syndrome:
1. MacrolidesIBA
2. Dyneins (Dynein)IBA
3. Matrix Metalloproteinases (MMPs)IBA
4. Retinaldehyde (Retinal)IBA
5. 23-valent pneumococcal capsular polysaccharide vaccineIBA
6. Anesthetics (Anesthetic Agents)IBA
7. Axonemal DyneinsIBA
8. Nitric Oxide (Nitrogen Monoxide)FDA Link
9. CarbohydratesIBA
10. BorohydridesIBA

Therapies and Procedures

1. Therapeutics
2. Analgesia
3. Segmental Mastectomy (Lumpectomy)
4. Lung Transplantation
5. Anesthesia