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Histidine Ammonia-Lyase

An enzyme that catalyzes the first step of histidine catabolism, forming UROCANIC ACID and AMMONIA from HISTIDINE. Deficiency of this enzyme is associated with elevated levels of serum histidine and is called histidinemia (AMINO ACID METABOLISM, INBORN ERRORS).
Also Known As:
Histidinase; Histidine Deaminase; Histidine alpha-Deaminase; Ammonia-Lyase, Histidine; Deaminase, Histidine; Histidine Ammonia Lyase; Histidine alpha Deaminase; alpha-Deaminase, Histidine; Histidase; L-Histidine ammonia-lyase
Networked: 63 relevant articles (0 outcomes, 8 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Azevedo, Cristina: 1 article (12/2021)
2. Denny, Paul W: 1 article (12/2021)
3. Docampo, Roberto: 1 article (12/2021)
4. Mantilla, Brian S: 1 article (12/2021)
5. Saiardi, Adolfo: 1 article (12/2021)
6. Alexander, Danny: 1 article (04/2015)
7. Bis, Joshua C: 1 article (04/2015)
8. Boerwinkle, Eric: 1 article (04/2015)
9. Dehghan, Abbas: 1 article (04/2015)
10. Franco, Oscar H: 1 article (04/2015)

Related Diseases

1. Histidinemia
2. Squamous Cell Carcinoma (Epidermoid Carcinoma)
3. Atherosclerosis
4. Skin Diseases (Skin Disease)
5. Schizophrenia (Dementia Praecox)

Related Drugs and Biologics

1. Enzymes
2. Histidine Ammonia-Lyase
3. Histidine (L-Histidine)
4. Urocanate Hydratase (Urocanase)
5. Xanthine Oxidase
6. Serotonin Antagonists
7. Ala(2)-Arg(6)- enkephalin-Leu
8. Urokinase-Type Plasminogen Activator (Urokinase)
9. Urocanic Acid
10. Proteins (Proteins, Gene)

Related Therapies and Procedures

1. Investigational Therapies (Experimental Therapy)