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Hemochromatosis (Bronze Diabetes)

A disorder of iron metabolism characterized by a triad of HEMOSIDEROSIS; LIVER CIRRHOSIS; and DIABETES MELLITUS. It is caused by massive iron deposits in parenchymal cells that may develop after a prolonged increase of iron absorption. (Jablonski's Dictionary of Syndromes & Eponymic Diseases, 2d ed)
Also Known As:
Bronze Diabetes; Hemochromatoses; Bronzed Cirrhosis; Familial Hemochromatosis; Genetic Hemochromatosis; Haemochromatosis; Iron Storage Disorder; Pigmentary Cirrhosis; Primary Hemochromatosis; Troisier-Hanot-Chauffard Syndrome; Von Recklenhausen-Applebaum Disease; Bronzed Cirrhoses; Cirrhoses, Bronzed; Cirrhoses, Pigmentary; Cirrhosis, Bronzed; Cirrhosis, Pigmentary; Disease, Von Recklenhausen-Applebaum; Diseases, Von Recklenhausen-Applebaum; Disorder, Iron Storage; Disorders, Iron Storage; Familial Hemochromatoses; Genetic Hemochromatoses; Haemochromatoses; Hemochromatose; Hemochromatoses, Familial; Hemochromatoses, Genetic; Hemochromatosis, Familial; Hemochromatosis, Genetic; Iron Storage Disorders; Pigmentary Cirrhoses; Recklenhausen-Applebaum Disease, Von; Recklenhausen-Applebaum Diseases, Von; Storage Disorder, Iron; Storage Disorders, Iron; Syndrome, Troisier-Hanot-Chauffard; Syndromes, Troisier-Hanot-Chauffard; Troisier Hanot Chauffard Syndrome; Troisier-Hanot-Chauffard Syndromes; Von Recklenhausen Applebaum Disease; Von Recklenhausen-Applebaum Diseases; Diabetes, Bronze
Networked: 4165 relevant articles (87 outcomes, 402 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Iron Overload
2. Fibrosis (Cirrhosis)
3. Anemia
4. Infections
5. Heart Failure

Experts

1. Barton, James C: 58 articles (06/2022 - 10/2002)
2. Adams, Paul C: 49 articles (01/2018 - 07/2002)
3. Powell, Lawrie W: 42 articles (01/2022 - 02/2002)
4. Brissot, Pierre: 41 articles (10/2022 - 01/2000)
5. Olynyk, John K: 39 articles (01/2022 - 04/2002)
6. Ganz, Tomas: 39 articles (06/2021 - 10/2002)
7. Acton, Ronald T: 38 articles (06/2022 - 10/2002)
8. Deugnier, Yves: 36 articles (11/2022 - 01/2000)
9. McLaren, Christine E: 36 articles (11/2020 - 02/2003)
10. Nemeth, Elizabeta: 32 articles (06/2021 - 02/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hemochromatosis:
1. IronIBA
2. Ferritins (Ferritin)IBA
3. Transferrin (beta 2 Transferrin)IBA
4. Deferoxamine (Desferal)FDA LinkGeneric
5. HepcidinsIBA
6. Chelating AgentsIBA
7. metal transporting protein 1 (ferroportin)IBA
8. Glucose (Dextrose)FDA LinkGeneric
9. Messenger RNA (mRNA)IBA
10. ErythropoietinFDA Link

Therapies and Procedures

1. Therapeutics
2. Liver Transplantation
3. Chelation Therapy (Therapy, Chelation)
4. Blood Transfusion (Blood Transfusions)
5. Aftercare (After-Treatment)