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Glycogen Debranching Enzyme System (Glycogen Debranching Enzyme)

1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
Also Known As:
Glycogen Debranching Enzyme; Debranching Enzyme, Glycogen; Enzyme, Glycogen Debranching; Transfer Glucosidase; Transfer-Glucosidase
Networked: 57 relevant articles (0 outcomes, 1 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Okubo, Minoru: 7 articles (02/2015 - 01/2002)
2. Murase, Toshio: 5 articles (11/2009 - 01/2002)
3. Comi, G P: 4 articles (03/2012 - 12/2002)
4. Ebara, Tetsu: 4 articles (11/2009 - 01/2005)
5. Shin, Yoon S: 4 articles (11/2009 - 01/2005)
6. Abdelhak, Sonia: 3 articles (07/2013 - 03/2012)
7. Tebib, Neji: 3 articles (07/2013 - 03/2012)
8. Kishnani, Priya S: 3 articles (11/2012 - 03/2007)
9. Aoyama, Yoshiko: 3 articles (11/2009 - 01/2005)
10. Endo, Yoriko: 3 articles (10/2007 - 01/2005)

Related Diseases

1. Stroke (Strokes)
2. Glycogen Storage Disease Type III (Cori's Disease)
3. Glycogen Storage Disease (Glycogenosis)
4. Myocardial Infarction
5. Hypoglycemia (Reactive Hypoglycemia)

Related Drugs and Biologics

1. Glycogen
2. Glycogen Phosphorylase (Phosphorylase, Glycogen)
3. amylo-1,6-glucosidase
4. Glucosidases
5. alpha-Glucosidases (Acid Maltase)
6. N-methyldeoxynojirimycin
7. caloreen
8. Protein Isoforms (Isoforms)
9. Nonsense Codon (Nonsense Mutation)
10. Complementary DNA (cDNA)

Related Therapies and Procedures

1. Heterologous Transplantation (Xenotransplantation)