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Glycogen Debranching Enzyme System (Glycogen Debranching Enzyme)

1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
Also Known As:
Glycogen Debranching Enzyme; Debranching Enzyme, Glycogen; Enzyme, Glycogen Debranching; Transfer Glucosidase; Transfer-Glucosidase
Networked: 82 relevant articles (0 outcomes, 2 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Okubo, Minoru: 7 articles (02/2015 - 01/2002)
2. Guin, Sunny: 6 articles (03/2018 - 04/2014)
3. Kishnani, Priya S: 5 articles (09/2020 - 03/2007)
4. Theodorescu, Dan: 5 articles (03/2018 - 04/2014)
5. Murase, Toshio: 5 articles (11/2009 - 01/2002)
6. Comi, G P: 4 articles (03/2012 - 12/2002)
7. Ebara, Tetsu: 4 articles (11/2009 - 01/2005)
8. Shin, Yoon S: 4 articles (11/2009 - 01/2005)
9. Sun, Baodong: 3 articles (09/2020 - 11/2012)
10. Weinhaus, Benjamin: 3 articles (03/2018 - 01/2016)

Related Diseases

1. Glycogen Storage Disease Type III (Cori's Disease)
2. Urinary Bladder Neoplasms (Bladder Cancer)
3. Ischemic Stroke
4. Glycogen Storage Disease (Glycogenosis)
5. Glycogen Storage Disease IIIA

Related Drugs and Biologics

1. Glycogen
2. Glycogen Phosphorylase (Phosphorylase, Glycogen)
3. Enzymes
4. Dextrins
5. amylo-1,6-glucosidase
6. Proteins (Proteins, Gene)
7. Glucosidases
8. Messenger RNA (mRNA)
9. miglitol (Glyset)
10. N-methyldeoxynojirimycin