Glycogen Debranching Enzyme System (Glycogen Debranching Enzyme)
1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
Also Known As:
Glycogen Debranching Enzyme; Debranching Enzyme, Glycogen; Enzyme, Glycogen Debranching; Transfer Glucosidase; Transfer-Glucosidase
Networked: 82
relevant articles (0 outcomes,
2 trials/studies)
Bio-Agent Context: Research Results
Experts
1. | Okubo, Minoru:
7 articles
(02/2015 - 01/2002)
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2. | Guin, Sunny:
6 articles
(03/2018 - 04/2014)
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3. | Kishnani, Priya S:
5 articles
(09/2020 - 03/2007)
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4. | Theodorescu, Dan:
5 articles
(03/2018 - 04/2014)
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5. | Murase, Toshio:
5 articles
(11/2009 - 01/2002)
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6. | Comi, G P:
4 articles
(03/2012 - 12/2002)
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7. | Ebara, Tetsu:
4 articles
(11/2009 - 01/2005)
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8. | Shin, Yoon S:
4 articles
(11/2009 - 01/2005)
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9. | Sun, Baodong:
3 articles
(09/2020 - 11/2012)
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10. | Weinhaus, Benjamin:
3 articles
(03/2018 - 01/2016)
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