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Glucosylceramidase (Glucocerebrosidase)

A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in GAUCHER DISEASE. EC 3.2.1.45.
Also Known As:
Glucocerebrosidase; Acid beta-Glucosidase; Glucosylceramide beta-Glucosidase; Glucocerebroside beta-Glucosidase; Glucosyl Ceramidase; Glucosylsphingosine Glucosyl Hydrolase; beta-Glucocerebrosidase; Acid beta Glucosidase; Ceramidase, Glucosyl; Glucocerebroside beta Glucosidase; Glucosyl Hydrolase, Glucosylsphingosine; Glucosylceramide beta Glucosidase; Hydrolase, Glucosylsphingosine Glucosyl; beta Glucocerebrosidase; beta-Glucosidase, Acid; beta-Glucosidase, Glucocerebroside; beta-Glucosidase, Glucosylceramide; D-Glucosyl-N-acylsphingosine glucosylhydrolase
Networked: 1701 relevant articles (31 outcomes, 103 trials/studies)

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Bio-Agent Context: Research Results

Experts

1. Sidransky, Ellen: 86 articles (05/2022 - 01/2002)
2. Schapira, Anthony H V: 40 articles (01/2022 - 04/2012)
3. Grabowski, Gregory A: 31 articles (01/2018 - 01/2003)
4. Futerman, Anthony H: 29 articles (01/2022 - 11/2002)
5. Zimran, Ari: 27 articles (01/2022 - 01/2003)
6. Alcalay, Roy N: 26 articles (11/2022 - 02/2010)
7. Aerts, Johannes M F G: 22 articles (01/2022 - 01/2004)
8. Goker-Alpan, Ozlem: 22 articles (01/2022 - 01/2004)
9. Tayebi, Nahid: 22 articles (06/2021 - 08/2002)
10. Elstein, Deborah: 20 articles (11/2017 - 01/2003)

Related Diseases

1. Gaucher Disease (Gaucher's Disease)
2. Parkinsonian Disorders (Parkinsonism)
3. Parkinson Disease (Parkinson's Disease)
4. Neurologic Manifestations (Neurological Manifestations)
5. Lysosomal Storage Diseases (Lysosomal Storage Disease)

Related Drugs and Biologics

1. Mannose (D-Mannose)
2. imiglucerase
3. Enzymes
4. Synucleins
5. Glucosylceramides (Glucocerebrosides)
6. taliglucerase alfa
7. Phosphotransferases (Kinase)
8. Leucine (L-Leucine)
9. Lipids
10. alglucerase

Related Therapies and Procedures

1. Enzyme Replacement Therapy
2. Therapeutics
3. Intravenous Administration
4. Enzyme Therapy
5. Intravenous Infusions