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Factor XI Deficiency (Hemophilia C)

A hereditary deficiency of blood coagulation factor XI (also known as plasma thromboplastin antecedent or PTA or antihemophilic factor C) resulting in a systemic blood-clotting defect called hemophilia C or Rosenthal's syndrome, that may resemble classical hemophilia.
Also Known As:
Hemophilia C; Deficiency, Factor 11; Deficiency, Factor Eleven; Deficiency, Factor XI; Factor 11 Deficiency; Factor Eleven Deficiency; Plasma Thromboplastin Antecedent Deficiency; Rosenthal's Syndrome; Deficiencies, Factor 11; Deficiencies, Factor Eleven; Deficiencies, Factor XI; Factor 11 Deficiencies; Factor Eleven Deficiencies; Factor XI Deficiencies; Rosenthal Syndromes; Rosenthal's Syndromes; Rosenthals Syndrome; Syndrome, Rosenthal; Syndrome, Rosenthal's; Rosenthal Syndrome
Networked: 272 relevant articles (3 outcomes, 15 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hemophilia A (Haemophilia)
2. Hemorrhage
3. Factor XI Deficiency (Hemophilia C)
4. Thrombosis (Thrombus)
5. Wounds and Injuries (Trauma)

Experts

1. Seligsohn, Uri: 7 articles (05/2010 - 04/2002)
2. Salomon, Ophira: 6 articles (03/2016 - 06/2003)
3. Zivelin, Ariella: 6 articles (08/2015 - 04/2002)
4. Gailani, David: 5 articles (01/2020 - 07/2004)
5. Weitz, Jeffrey I: 3 articles (04/2021 - 05/2016)
6. Tamarin, Ilia: 3 articles (03/2016 - 01/2005)
7. Livnat, Tami: 3 articles (08/2015 - 06/2003)
8. Bauduer, F: 3 articles (07/2015 - 10/2004)
9. Franchini, Massimo: 3 articles (10/2011 - 10/2006)
10. Gailani, D: 3 articles (09/2006 - 10/2004)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Factor XI Deficiency:
1. Factor XI (Plasma Thromboplastin Antecedent)IBA
2. Factor IX (Coagulation Factor IX)FDA LinkGeneric
3. Immunoglobulins (Immunoglobulin)IBA
4. Adrenal Cortex Hormones (Corticosteroids)IBA
5. Anesthetics (Anesthetic Agents)IBA
6. AnticoagulantsIBA
7. ThrombinFDA Link
8. Hemostatics (Antihemorrhagics)IBA
9. Proteins (Proteins, Gene)FDA Link
10. Factor XIa (Coagulation Factor XIa)IBA

Therapies and Procedures

1. Liver Transplantation
2. Aftercare (After-Treatment)
3. Therapeutics
4. Operative Surgical Procedures
5. Plasma Exchange