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Factor V Deficiency

A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed)
Also Known As:
Deficiency, Factor 5; Deficiency, Factor Five; Deficiency, Factor V; Factor 5 Deficiency; Factor Five Deficiency; Labile Factor Deficiency; Owren Parahemophilia; Owren's Disease; Deficiencies, Factor 5; Deficiencies, Factor Five; Deficiencies, Factor V; Deficiencies, Labile Factor; Deficiency, Labile Factor; Disease, Owren; Disease, Owren's; Factor 5 Deficiencies; Factor Five Deficiencies; Factor V Deficiencies; Labile Factor Deficiencies; Owrens Disease; Parahemophilia, Owren; Parahemophilias; Owren Disease; Parahemophilia
Networked: 221 relevant articles (2 outcomes, 11 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hemorrhage
2. Hemophilia A (Haemophilia)
3. Activated Protein C Resistance (APC Resistance)
4. Factor VII Deficiency (Hypoproconvertinemia)
5. Disease Susceptibility (Diathesis)

Experts

1. Liras, Antonio: 4 articles (05/2022 - 09/2021)
2. Castoldi, E: 4 articles (01/2018 - 06/2001)
3. Asselta, R: 4 articles (06/2003 - 12/2000)
4. Duga, S: 4 articles (06/2003 - 12/2000)
5. Montefusco, M C: 4 articles (06/2003 - 12/2000)
6. Tenchini, M L: 4 articles (06/2003 - 12/2000)
7. De Pablo-Moreno, Juan A: 3 articles (05/2022 - 09/2021)
8. Wang, Mingshan: 3 articles (01/2021 - 04/2014)
9. Simioni, P: 3 articles (07/2018 - 05/2011)
10. Spiezia, L: 3 articles (07/2018 - 05/2011)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Factor V Deficiency:
1. Factor V (Coagulation Factor V)IBA
2. recombinant FVIIa (rFVIIa)FDA Link
3. Fibrinogen (Factor I)FDA Link
4. Oral ContraceptivesIBA
5. factor V clotting antigenIBA
6. Blood Coagulation Factors (Coagulation Factor)IBA
7. AnticoagulantsIBA
8. von Willebrand FactorIBA
9. Carrier Proteins (Binding Protein)IBA
10. Adrenal Cortex Hormones (Corticosteroids)IBA

Therapies and Procedures

1. Therapeutics
2. Platelet Transfusion (Blood Platelet Transfusions)
3. Operative Surgical Procedures
4. Renal Dialysis (Hemodialysis)
5. Liver Transplantation