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Ebstein Anomaly (Ebsteins Anomaly)

A congenital heart defect characterized by downward or apical displacement of the TRICUSPID VALVE, usually with the septal and posterior leaflets being attached to the wall of the RIGHT VENTRICLE. It is characterized by a huge RIGHT ATRIUM and a small and less effective right ventricle.
Also Known As:
Ebsteins Anomaly; Ebstein's Anomaly; Ebstein's Malformation; Familial Ebstein's Anomaly; Anomaly, Ebstein; Anomaly, Ebstein's; Ebstein Malformation; Ebstein's Anomaly, Familial; Ebsteins Malformation; Familial Ebstein Anomaly; Familial Ebsteins Anomaly; Malformation, Ebstein's
Networked: 323 relevant articles (12 outcomes, 17 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Atrial Heart Septal Defects (Atrial Septal Defect)
2. Tachycardia (Tachyarrhythmias)
3. Supraventricular Tachycardia
4. Pathologic Constriction (Stenosis)
5. Cardiomyopathies (Cardiomyopathy)

Experts

1. Dearani, Joseph A: 5 articles (01/2022 - 06/2012)
2. Moore, Jeremy P: 4 articles (01/2022 - 07/2017)
3. Walsh, Edward P: 4 articles (11/2021 - 10/2018)
4. Connolly, Heidi M: 4 articles (01/2021 - 06/2012)
5. Gatzoulis, Michael A: 3 articles (01/2022 - 06/2012)
6. McLeod, Christopher J: 3 articles (01/2022 - 01/2018)
7. Warnes, Carole A: 3 articles (01/2022 - 06/2012)
8. Gallotti, Roberto G: 3 articles (12/2019 - 07/2017)
9. Shannon, Kevin M: 3 articles (12/2019 - 07/2017)
10. Eicken, Andreas: 3 articles (10/2019 - 04/2015)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Ebstein Anomaly:
1. PlasticsIBA
2. Oxygen (Dioxygen)IBA
3. Dopamine (Intropin)FDA LinkGeneric
4. Amiodarone (Amiodarona)FDA LinkGeneric
5. Adenosine (Adenocard)FDA LinkGeneric
6. LithiumIBA
7. Myosin Heavy Chains (Myosin Heavy Chain)IBA
8. Anesthetics (Anesthetic Agents)IBA
9. Proteins (Proteins, Gene)FDA Link
10. Alprostadil (Muse)FDA LinkGeneric

Therapies and Procedures

1. Therapeutics
2. Fontan Procedure (Fontan Operation)
3. Radiofrequency Ablation
4. Bioprosthesis
5. Cardiac Resynchronization Therapy