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Ebstein Anomaly (Ebsteins Anomaly)

A congenital heart defect characterized by downward or apical displacement of the TRICUSPID VALVE, usually with the septal and posterior leaflets being attached to the wall of the RIGHT VENTRICLE. It is characterized by a huge RIGHT ATRIUM and a small and less effective right ventricle.
Also Known As:
Ebsteins Anomaly; Ebstein's Anomaly; Ebstein's Malformation; Familial Ebstein's Anomaly; Anomaly, Ebstein; Anomaly, Ebstein's; Ebstein Malformation; Ebstein's Anomaly, Familial; Ebsteins Malformation; Familial Ebstein Anomaly; Familial Ebsteins Anomaly; Malformation, Ebstein's
Networked: 231 relevant articles (5 outcomes, 10 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Atrial Heart Septal Defects (Atrial Septal Defect)
2. Tachycardia (Tachyarrhythmias)
3. Pathologic Constriction (Stenosis)
4. Pulmonary Valve Stenosis (Pulmonary Stenosis)
5. Pulmonary Atresia (Pulmonary Valve Atresia)

Experts

1. McElhinney, Doff B: 3 articles (04/2015 - 11/2003)
2. Wise, Linda J: 2 articles (09/2015 - 09/2015)
3. Bhatia, Jatinder: 2 articles (09/2015 - 09/2015)
4. Walters, Kenneth C: 2 articles (09/2015 - 09/2015)
5. Ham, Phillip Benson: 2 articles (09/2015 - 09/2015)
6. Stansfield, Brian: 2 articles (09/2015 - 09/2015)
7. Wang, Eric J: 2 articles (09/2015 - 09/2015)
8. Hatley, Robyn M: 2 articles (09/2015 - 09/2015)
9. Pipkin, Walter L: 2 articles (09/2015 - 09/2015)
10. Hörer, Jürgen: 2 articles (04/2015 - 01/2010)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Ebstein Anomaly:
1. OxygenIBA
2. Dopamine (Intropin)FDA LinkGeneric
3. LithiumIBA
4. Myosin Heavy Chains (Myosin Heavy Chain)IBA
5. tranilast (N 5')IBA
08/15/2005 - "From 1984 to 2004, 66 patients were diagnosed with Ebstein's malformation (n = 61) or congenital tricuspid valve (TV) dysplasia (n = 5) in utero or during the first month of life. "
11/01/1989 - "To determine which morphologic features are associated with early death, the complete echocardiograms and medical records of 16 consecutive patients with Ebstein's anomaly and concordant atrioventricular connections who presented in the fetal (n = 5) or neonatal (n = 11) period were reviewed. "
07/01/2009 - "Thirty-six patients (78%) had associated cardiac lesions, including atrial septal defect (n = 16 [35%]), ventricular septal defect (n = 17 [37%]), patent ductus arteriosus (n = 14 [30%]), and Ebstein's anomaly (n = 5 [11%]). "
07/01/1996 - "1994 50 neonates underwent cardiac surgery using CPB (n = 23 transposition of the great arteries; n = 4 pulmonary atresia; n = 6 critical pulmonary stenosis; n = 5 hypoplastic left heart syndrome; n = 3 Ebstein's anomaly; n = 2 interrupted arch with hypoplastic left ventricle; n = 2 single ventricle; n = 1 each: double outlet right ventricle, tricuspid atresia, critical aortic stenosis, rhabdo-myosarkoma, corrected transposition of the great arteries.) Thirty-one patients entered the study. "
09/15/1993 - "Since 1990, radiofrequency ablation of accessory atrioventricular (AV) pathways has been attempted in 10 patients (age range 3.5 months to 30 years) with congenital heart disease: Ebstein's anomaly (n = 5), heterotaxy with AV discordance (n = 3), tetralogy of Fallot (n = 1) and total anomalous pulmonary venous return (n = 1). "
6. Alprostadil (Muse)FDA LinkGeneric
7. Phenobarbital (Luminal)FDA Link
8. Coarctation of the aortaIBA
9. Pulmonary venous return anomalyIBA
10. Complete atrioventricular septal defectIBA

Therapies and Procedures

1. Fontan Procedure (Fontan Operation)
2. Bioprosthesis
3. Cryosurgery
4. Catheters
5. Right Heart Bypass (Cavopulmonary Anastomosis)