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Double Outlet Right Ventricle

Incomplete transposition of the great vessels in which both the AORTA and the PULMONARY ARTERY arise from the RIGHT VENTRICLE. The only outlet of the LEFT VENTRICLE is a large ventricular septal defect (VENTRICULAR SEPTAL DEFECTS or VSD). The various subtypes are classified by the location of the septal defect, such as subaortic, subpulmonary, or noncommitted.
Also Known As:
Double Outlet Right Ventricle, Noncommitted VSD; Double Outlet Right Ventricle, Subaortic VSD; Double Outlet Right Ventricle, Subpulmonary VSD; Anomaly, Taussig-Bing; Taussig Bing Anomaly; Taussig-Bing Anomaly
Networked: 250 relevant articles (2 outcomes, 13 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Pulmonary Valve Stenosis (Pulmonary Stenosis)
2. Ventricular Heart Septal Defects (Ventricular Septal Defect)
3. Tetralogy of Fallot (Fallot Tetralogy)
4. Pulmonary Atresia (Pulmonary Valve Atresia)
5. Tricuspid Atresia

Experts

1. Liu, Ying-Long: 3 articles (07/2010 - 06/2008)
2. Aoki, Mitsuru: 3 articles (11/2008 - 03/2002)
3. Bacha, Emile A: 3 articles (07/2006 - 01/2003)
4. Shinoka, Toshiharu: 2 articles (09/2015 - 03/2002)
5. Lin, Angela E: 2 articles (10/2014 - 04/2011)
6. Sekarski, Nicole: 2 articles (06/2014 - 10/2004)
7. Lee, Chang-Ha: 2 articles (03/2012 - 02/2007)
8. Lee, Cheul: 2 articles (03/2012 - 02/2007)
9. Kwak, Jae Gun: 2 articles (03/2012 - 02/2007)
10. Tantchou Tchoumi, J C: 2 articles (03/2011 - 02/2011)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Double Outlet Right Ventricle:
1. Staphylococcal Protein A (A, Protein)IBA
2. Complete atrioventricular septal defectIBA
3. tranilast (N 5')IBA
05/01/2001 - "Common heart defects were aortic atresia (n = 8), mitral atresia and double-outlet right ventricle (n = 5), and unbalanced AVC (n = 5). "
01/01/1984 - ""Complicated" VSD in terms of muscular/multiple (n = 6), subaortic type of double-outlet right ventricle (n = 5), AV-canal type (n = 2) and straddling chordae (n = 2) was present in 15 cases. "
02/01/1994 - "Associated cardiac lesions included double-inlet left ventricle anatomy (n = 5), double-outlet right ventricle (n = 4), abnormal aortic valve (n = 5), unbalanced atrioventricular canal (n = 3), and membranous ventricular septal defect (n = 1). "
10/01/1993 - "The primary diagnoses were transposition of the great arteries with ventricular septal defect (n = 10), transposition of the great arteries with intact ventricular septum (n = 5), Taussig-Bing anomaly (n = 4), and atrioventricular and ventriculoarterial discordance (n = 5). "
06/01/2009 - "Fourteen patients were candidates for terminal biventricular repair [atrioventricular septal defect (AVSD) (n=6), double outlet right ventricle (DORV) +ventricular septal defect (VSD) (n=4), Swiss cheese VSD (n=2), transposition of the great arteries (TGA) +Swiss cheese VSD (n=1), ASD+VSD+aortic coarctation (n=1)], and the remaining 14 were candidates for terminal univentricular repair [double inlet left ventricle (n=5), double inlet right ventricle (n=2), AVSD+left ventricular (LV) hypoplasia (n=2), DORV+LV hypoplasia (n=2); tricuspid atresia (n=1), left AV valve atresia (n=1), TGA+Swiss cheese VSD+LV hypoplasia (n=1). "
4. Congenitally corrected transposition of the great arteriesIBA
5. Coarctation of the aortaIBA
6. Tretinoin (Retinoic Acid)FDA LinkGeneric
7. Right ventricle hypoplasiaIBA
8. Myosin Type IIIBA
9. Transcription Factors (Transcription Factor)IBA
10. AntibodiesIBA

Therapies and Procedures

1. Blalock-Taussig Procedure
2. Fontan Procedure (Fontan Operation)
3. Homologous Transplantation (Allograft)
4. Transplants (Transplant)
06/01/2014 - "One hundred and six Contegra grafts were implanted between April 1999 and April 2010 for the Ross procedure (n = 46), isolated pulmonary valve replacement (n = 32), tetralogy of Fallot (n = 24), double-outlet right ventricle (n = 7), troncus arteriosus (n = 4), switch operation (n = 1) and redo of pulmonary valve replacement (n = 2). "
04/01/2011 - "All patients had normal ventricular function at latest echocardiography and were in NYHA class 1. The arterial switch operation in Transposition of Great Arteries or Double Outlet Right Ventricle patients with intramural coronary can be performed with low mortality; however, there is a high incidence of intraoperative or postoperative coronary problems, which can be managed with conversion to the individual coronary button technique and a bypass procedure using a left subclavian free graft. "
07/01/2005 - "We report a case of congenital ascending aortic aneurysm associated with double-outlet right ventricle that has been successfully repaired by graft replacement and extracardiac total cavo-pulmonary connection."
09/01/1975 - "Subsequently a transverse right ventriculotomy, either alone or combined with a right ventricular outflow and/or pulmonary artery patch enlargement was performed in 16 patients, and a double outlet right ventricle was created through insertion of a Dacron tube graft in two patients. "
07/01/1992 - "The diagnosis was transposition of the great arteries with ventricular septal defect and left ventricular outflow tract obstruction in 51, truncus arteriosus in 36, pulmonary atresia with ventricular septal defect in 25, tetralogy of Fallot in 19, double-outlet right ventricle in 10, pulmonary atresia with intact ventricular septum in 6 and atrioventricular canal with pulmonary atresia in 1. A Dacron porcine-valved conduit was used in 37, a homograft conduit in 106 and a nonvalved conduit in 5. There were 13 early deaths overall (8.8%); 8 (22%) of the early deaths occurred in the 37 patients who received a Dacron graft, 4 (3.8%) occurred in the 106 patients who received a homograft and 1 occurred in a patient with a nonvalved Gore-Tex conduit. "
5. Right Heart Bypass (Cavopulmonary Anastomosis)