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Dandy-Walker Syndrome (Dandy Walker Malformation)

A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)
Also Known As:
Dandy Walker Malformation; Dandy-Walker Complex; Dandy-Walker Cyst; Dandy-Walker Deformity; Dandy-Walker Syndrome, Familial; Hydrocephalus, Internal, Dandy-Walker Type; Hydrocephalus, Noncommunicating, Dandy-Walker Type; Luschka-Magendie Foramina Atresia; Cyst, Dandy-Walker; Cysts, Dandy-Walker; Dandy Walker Complex; Dandy Walker Deformity; Dandy Walker Syndrome; Dandy Walker Syndrome, Familial; Dandy-Walker Complices; Dandy-Walker Cysts; Dandy-Walker Deformities; Familial Dandy-Walker Syndrome; Luschka Magendie Foramina Atresia; Malformation, Dandy-Walker; Dandy-Walker Malformation
Networked: 118 relevant articles (2 outcomes, 5 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Hydrocephalus (Hydrocephaly)
2. Cysts
3. Subdural Effusion (Subdural Hygroma)
4. Hematoma
5. Dandy Walker variant

Experts

1. Pilu, G: 5 articles (07/2016 - 06/2012)
2. Volpe, G: 4 articles (10/2021 - 06/2012)
3. Volpe, P: 4 articles (10/2021 - 06/2012)
4. Ghi, T: 4 articles (01/2021 - 06/2012)
5. Lerman-Sagie, T: 3 articles (07/2016 - 11/2014)
6. Contro, E: 3 articles (02/2014 - 06/2012)
7. Limbrick, David D: 2 articles (11/2021 - 04/2021)
8. De Robertis, V: 2 articles (10/2021 - 02/2014)
9. Rozzelle, Curtis J: 2 articles (04/2021 - 04/2014)
10. Donarini, G: 2 articles (08/2019 - 06/2019)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Dandy-Walker Syndrome:
1. Radioisotopes (Radionuclides)IBA
2. Anesthetics (Anesthetic Agents)IBA
3. NestinIBA
4. Warfarin (Coumadin)FDA LinkGeneric
5. VimentinIBA
6. Immune Sera (Antisera)IBA
7. Glial Fibrillary Acidic ProteinIBA
8. Genetic Markers (Genetic Marker)IBA
9. cytidylyl-(3'-5')-cytidine (CpC)IBA
10. A 17 (A-17)IBA

Therapies and Procedures

1. Colonic Pouches (S Pouch)
2. Ventriculostomy
3. Therapeutics
4. Ventriculoperitoneal Shunt
5. Catheters