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Hereditary Nonpolyposis Colorectal Neoplasms (Hereditary Nonpolyposis Colorectal Cancer)

A group of autosomal-dominant inherited diseases in which COLON CANCER arises in discrete adenomas. Unlike FAMILIAL POLYPOSIS COLI with hundreds of polyps, hereditary nonpolyposis colorectal neoplasms occur much later, in the fourth and fifth decades. HNPCC has been associated with germline mutations in mismatch repair (MMR) genes. It has been subdivided into Lynch syndrome I or site-specific colonic cancer, and LYNCH SYNDROME II which includes extracolonic cancer.
Also Known As:
Hereditary Nonpolyposis Colorectal Cancer; Colon Cancer, Familial Nonpolyposis; Syndrome, Lynch; Lynch Syndrome; Familial Nonpolyposis Colon Cancer; Colorectal Neoplasms, Hereditary Nonpolyposis; Colorectal Cancer Hereditary Nonpolyposis; Hereditary Nonpolyposis Colon Cancer; Lynch Cancer Family Syndrome I; Lynch Syndrome I; Colon Cancer, Familial Nonpolyposis, Type 1; Colorectal Cancer, Hereditary Nonpolyposis, Type 1; Familial Nonpolyposis Colon Cancer Type 1; Hereditary Nonpolyposis Colorectal Cancer Type 1
Networked: 1234 relevant articles (33 outcomes, 112 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Neoplasms (Cancer)
2. Colorectal Neoplasms (Colorectal Cancer)
3. Microsatellite Instability
4. Endometrial Neoplasms (Endometrial Cancer)
5. Turcot syndrome

Experts

1. Kloor, Matthias: 23 articles (01/2022 - 05/2005)
2. Jenkins, Mark A: 23 articles (01/2021 - 09/2005)
3. Hampel, Heather: 22 articles (01/2020 - 07/2004)
4. Hopper, John L: 21 articles (01/2021 - 09/2005)
5. Thibodeau, Stephen N: 21 articles (01/2021 - 07/2004)
6. Boland, C Richard: 20 articles (01/2022 - 01/2005)
7. Buchanan, Daniel D: 20 articles (11/2020 - 03/2008)
8. Lindor, Noralane M: 18 articles (01/2021 - 04/2005)
9. von Knebel Doeberitz, Magnus: 17 articles (10/2021 - 09/2006)
10. Mecklin, Jukka-Pekka: 17 articles (01/2021 - 10/2005)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hereditary Nonpolyposis Colorectal Neoplasms:
1. Immune Checkpoint InhibitorsIBA
2. Calcibiotic Root Canal SealerIBA
3. pembrolizumabIBA
4. Aspirin (Acetylsalicylic Acid)FDA LinkGeneric
5. VaccinesIBA
6. Proteins (Proteins, Gene)FDA Link
7. Biomarkers (Surrogate Marker)IBA
8. CalciumIBA
9. Fluorouracil (Carac)FDA LinkGeneric
10. Capsules (Microcapsules)IBA

Therapies and Procedures

1. Therapeutics
2. Immunotherapy
3. Colectomy
4. Chemoprevention
5. Hysterectomy