|1.||Zerr, Inga: 10 articles (11/2014 - 01/2002)|
|2.||Kitamoto, Tetsuyuki: 9 articles (08/2015 - 12/2003)|
|3.||Yamada, Masahito: 8 articles (08/2015 - 11/2003)|
|4.||Mizusawa, Hidehiro: 7 articles (08/2015 - 11/2008)|
|5.||Mead, Simon: 7 articles (11/2014 - 03/2008)|
|6.||Collinge, John: 7 articles (11/2014 - 12/2004)|
|7.||Gambetti, Pierluigi: 6 articles (01/2015 - 01/2003)|
|8.||Kim, Yong-Sun: 6 articles (01/2014 - 02/2010)|
|9.||Budka, Herbert: 6 articles (12/2013 - 05/2003)|
|10.||Kovacs, Gabor G: 5 articles (08/2015 - 05/2003)|
|1.||Creutzfeldt-Jakob Syndrome (Creutzfeldt-Jakob Disease)
01/01/2013 - "Here, we review the results of the recent high-resolution nuclear magnetic resonance (NMR) structural studies on HuPrPs with pathological Q212P and V210I mutations linked with Gerstmann-Sträussler-Scheinker (GSS) syndrome and familial Creutzfeldt-Jakob disease (fCJD), respectively, and HuPrP carrying naturally occurring E219K polymorphism considered to protect against sporadic CJD (sCJD). "
07/01/2011 - "Human genome wide association has been done in variant Creutzfeldt-Jakob disease (CJD) and are ongoing in larger collections of sporadic CJD with findings around, but not clearly beyond, the levels of statistical significance required in these studies (THRB-RARB, STMN2). "
01/01/2011 - "The E200K mutation is the most frequent prion protein gene (PRNP) mutation detected worldwide that is associated with Creutzfeldt-Jakob disease (CJD) and thought to have overlapping features with sporadic CJD, yet detailed neuropathological studies have not been reported. "
08/01/2015 - "It has long been recognized that 129M/M homozygotes are overrepresented in sporadic Creutzfeldt-Jakob disease (CJD) patients and variant CJD patients, whereas 219E/K heterozygotes are absent in sporadic CJD patients. "
08/01/2009 - "We report here an autopsy case of sporadic Creutzfeldt-Jakob disease (CJD) without hereditary burden and with a clinical course typical of sporadic CJD. "
|2.||Prion Diseases (Transmissible Spongiform Encephalopathies)
08/01/2015 - "For example, although 219E/K heterozygosity confers resistance against the development of sporadic CJD, this genotype is not entirely protective against acquired forms (iatrogenic CJD and variant CJD) or genetic forms (genetic CJD and Gerstmann-Sträussler-Scheinker syndrome) of prion diseases. "
10/19/2012 - "The results of this study will aid in the design of diagnostic assays that can detect prion disease across the diversity of sporadic CJD subtypes."
02/01/2010 - "Our study about distinct prevalence patterns of HERVs reflects that some HERVs families may be associated with the development of prion diseases, and considered as a candidate marker for the diagnosis of sporadic CJD."
04/01/2014 - "Among National Prion Clinic referrals in whom a prion disease diagnosis was likely, 2 patients with sporadic CJD tested positive (98.1% specificity; 95% CI, 93.3%-99.8%). "
04/01/2014 - "Isolates from sporadic CJD, the most common form of prion disease, showed the highest sensitivity. "
|3.||Bovine Spongiform Encephalopathy (Mad Cow Disease)
08/01/1996 - "As bovine spongiform encephalopathy (BSE) has not been reported in Austria, the data do not support a link between a rise in incidence of sporadic CJD and BSE."
05/10/2005 - "Intercountry comparisons did not suggest any relative change in the characteristics of sporadic CJD in the United Kingdom, and the evidence in this study does not suggest the occurrence of a novel form of human bovine spongiform encephalopathy infection other than variant CJD. "
06/19/2001 - "Such studies have shown that the bovine spongiform encephalopathy (BSE) agent is indistinguishable from the agent causing variant Creutzfeldt-Jakob disease (vCJD), but differs from isolates of sporadic CJD, reinforcing the idea that the vCJD epidemic in Britain results from consumption of contaminated beef products. "
11/03/2000 - "Thus less virulent sporadic CJD infections in older people can conceal other agents such as variant CJD, the more recently evolved and virulent agent linked to bovine spongiform encephalopathy. "
04/01/2004 - "Variant CJD, related to bovine spongiform encephalopathy, shows a different clinical course, symmetrical high intensity MRI signal in the pulvinar, presence of PrPSc in tonsil biopsy tissue, and a lower sensitivity of CSF 14-3-3 protein compared to sporadic CJD. "
08/01/2015 - "Atypical sporadic CJD-MM phenotype with white matter kuru plaques associated with intranuclear inclusion body and argyrophilic grain disease."
01/01/2014 - "The other SNP of the gene that encodes SCG10 (STMN2), which is related to clinical onset of sporadic CJD, was also associated with variant CJD and kuru. "
05/01/2011 - "Murine adapted human agents, including sporadic CJD (sCJD), New Guinea kuru, and Japanese CJD agents, display particularly distinct incubation times and maximal infectious brain titers. "
12/01/2010 - "In 2 cases of sporadic CJD, the kuru stellate plaque predominated."
08/11/2009 - "Many TSE agents can infect monotypic cultured GT1 cells, and unlike sporadic CJD isolates, kuru rapidly and stably infected these cells. "
12/01/2009 - "In our study we have compared prion characteristics of different forms of sheep scrapie with those of different phenotypes of sporadic CJD. "
12/01/2009 - "The same applies to sporadic CJD type 2 and classical scrapie. "
12/01/2009 - "The disease characteristics of sporadic CJD depend considerably on the prion type 1 or 2. Our results show that there are obvious parallels between sporadic CJD type 1 and the so-called atypical/Nor98 scrapie. "
09/01/2005 - "Although the lymphoreticular system is involved in the earlier pathogenesis of some forms of sheep scrapie and vCJD, which presents great opportunity for diagnostic development, other TSE diseases (some strains of scrapie, sporadic CJD (sCJD) and bovine BSE) do not present such a diagnostic opportunity. "
01/01/2003 - "In contrast, different TSE strains are associated with sporadic CJD and sheep scrapie."
|1.||Amyloid (Amyloid Fibrils)
|5.||14-3-3 Proteins (14-3-3 Protein)
|6.||Proteins (Proteins, Gene)
|9.||Aquaporins (Water Channels)
|1.||Blood Transfusion (Blood Transfusions)