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Amyopathic dermatomyositis

Dermatomyositis with pathognomonic cutaneous manifestations of dermatomyositis, consisting of a heliotrope rash, facial erythema and edema, Gottron's papules, and periungual TELANGIECTASIA, but without inflammatory myopathy features. Patients usually do not have muscle weakness, but may present with minor muscle abnormalities
Networked: 201 relevant articles (7 outcomes, 6 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Interstitial Lung Diseases (Interstitial Lung Disease)
2. Dermatomyositis (Dermatopolymyositis)
3. Melanoma (Melanoma, Malignant)
4. Polymyositis
5. Fever (Fevers)

Experts

1. Kuwana, Masataka: 9 articles (01/2022 - 05/2005)
2. Mimori, Tsuneyo: 8 articles (09/2019 - 05/2005)
3. Sato, Shinji: 7 articles (01/2022 - 05/2005)
4. Guo, Qiang: 7 articles (01/2021 - 08/2014)
5. Bao, Chunde: 6 articles (01/2021 - 08/2014)
6. Nakashima, Ran: 6 articles (09/2019 - 11/2007)
7. Hosono, Yuji: 5 articles (09/2019 - 06/2012)
8. Okiyama, Naoko: 4 articles (10/2022 - 11/2016)
9. Fujimoto, Manabu: 4 articles (12/2021 - 04/2013)
10. Takada, Toshinori: 4 articles (01/2018 - 09/2015)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Amyopathic dermatomyositis:
1. Cyclosporine (Ciclosporin)FDA LinkGeneric
2. tofacitinibIBA
3. Ligases (Synthetase)IBA
01/01/2023 - "We genotyped and compared the minor allele A frequency of WDFY4 rs7919656 in patients with MDA5+DM (n = 254) including 190 clinically amyopathic dermatomyositis (CADM), MDA5-DM (n = 53), anti-synthetases syndrome (ASyS, n = 72) and healthy controls (n = 192). "
10/22/2018 - "Therefore, the goal of the present study was to evaluate the safety and efficacy of MMF (monotherapy or coadjuvant drug) in a specific sample of patients with refractory SAM: dermatomyositis, polymyositis, anti-synthetase syndrome or clinically amyopathic dermatomyositis. "
09/01/2019 - "Of the 32 anti-MDA5 antibody-positive patients, eleven patients were clinically diagnosed with interstitial pneumonia with autoimmune features (IPAF), ten patients were diagnosed with clinically amyopathic dermatomyositis (CADM), six patients were diagnosed with dermatomyositis (DM) and five patients were diagnosed with anti-synthetase syndrome (ASS). "
01/01/2017 - "Dermatomyositis subdivides into various clinical forms such as juvenile, amyopathic or paraneoplastic dermatomyositis, scleromyositis, overlap or anti-synthetase syndromes, etc. Recently, numerous new antibodies defining the characteristic clinical phenotype have been described as anti-MDA5 antibodies associated with interstitial lung disease and amyopathic dermatomyositis or anti-TIF1γ antibodies as markers for paraneoplastic dermatomyositis. "
11/01/2014 - "Amyopathic dermatomyositis associated with anti-MDA5 autoantibodies shares some characteristics with those associated with anti-synthetase antibodies. "
4. AutoantibodiesIBA
5. Cyclophosphamide (Cytoxan)FDA LinkGeneric
6. Adrenal Cortex Hormones (Corticosteroids)IBA
7. Immunosuppressive Agents (Immunosuppressants)IBA
8. SteroidsIBA
9. pirfenidoneIBA
10. Janus Kinase InhibitorsIBA

Therapies and Procedures

1. Therapeutics
2. Blood Component Removal (Apheresis)
3. Plasma Exchange
4. Hemoperfusion
5. Extracorporeal Membrane Oxygenation