familial British Dementia

Also Known As:
Dementia, familial British; Cerebral amyloid angiopathy, British type; Presenile dementia with spastic ataxia
Networked: 29 relevant articles (0 outcomes, 0 trials/studies)

Bio-Agent Context: Research Results


1. Plant, G: 5 articles (11/2001 - 01/2000)
2. Frangione, B: 5 articles (11/2001 - 01/2000)
3. Ghiso, Jorge: 4 articles (12/2014 - 07/2002)
4. Vidal, R: 4 articles (11/2001 - 01/2000)
5. Rostagno, A: 4 articles (11/2001 - 01/2000)
6. Ghiso, J: 4 articles (02/2001 - 01/2000)
7. Rostagno, Agueda: 3 articles (12/2014 - 07/2002)
8. Revesz, Tamas: 3 articles (05/2013 - 07/2002)
9. Lashley, Tammaryn: 3 articles (05/2013 - 07/2002)
10. Revesz, T: 3 articles (11/2001 - 05/2000)

Related Diseases

1. Neurodegenerative Diseases (Neurodegenerative Disease)
2. Alzheimer Disease (Alzheimer's Disease)
3. Amyloid Plaque
4. Dementia (Dementias)
5. Prion Diseases (Transmissible Spongiform Encephalopathies)
09/01/2002 - "In addition to AD, an increasing number of neurodegenerative disorders, including Parkinson's disease, familial British dementia, familial amyloid polyneuropathy, amyotrophic lateral sclerosis, and prion diseases, are associated with abnormal protein assembly processes. "
07/01/2002 - "CAA occurs in several familial conditions, including hereditary cerebral hemorrhage with amyloidosis of Icelandic type caused by deposition of mutant cystatin C, hereditary cerebral hemorrhage with amyloidosis Dutch type and familial AD with deposition of either A beta variants or wild-type A beta, the transthyretin-related meningo-vascular amyloidoses, gelsolin as well as familial prion disease-related CAAs and the recently described BRI2 gene-related CAAs in familial British dementia and familial Danish dementia. "
12/01/2008 - "Using a method based on ESR spectroscopy and spin-trapping, we have shown that Abeta (amyloid beta-peptide) (implicated in Alzheimer's disease), alpha-synuclein (implicated in Parkinson's disease), ABri (British dementia peptide) (responsible for familial British dementia), certain toxic fragments of the prion protein (implicated in the transmissible spongiform encephalopathies) and the amylin peptide (found in the pancreas in Type 2 diabetes mellitus) all have the common ability to generate H(2)O(2) in vitro. "
07/01/2009 - "These latter proteins include the ABri and ADan subunits in familial British dementia and familial Danish dementia, respectively, which are also known under the umbrella term BRI2 gene-related dementias, variant cystatin C in hereditary cerebral haemorrhage with amyloidosis of Icelandic-type, variant transthyretins in meningo-vascular amyloidosis, disease-associated prion protein (PrP(Sc)) in hereditary prion disease with premature stop codon mutations and mutated gelsolin (AGel) in familial amyloidosis of Finnish type. "

Related Drugs and Biologics

1. familial Danish Dementia
2. Amyloid (Amyloid Fibrils)
3. Peptides
4. Cystatin C
5. Gelsolin
6. Amyloid angiopathy
7. Islet Amyloid Polypeptide
8. Presenilin-2
9. Presenilin-1
10. alpha-Synuclein