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bilateral Multicystic renal dysplasia

A lethal form of multicystic dysplastic kidney disease that usually presents before birth by ultrasound imaging of the fetus. Both kidneys are large due to multiple cysts and non-functional. It is caused by mutations in the TBX18 gene. OMIM: 143400
Also Known As:
Multicystic renal dysplasia, bilateral; Hydronephrosis Due To Pujo; Pelvi-ureteric junction obstruction; Pelviureteric Junction Obstruction
Networked: 66 relevant articles (2 outcomes, 6 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1. Convalescence
2. Ureterocele
3. Urolithiasis
4. Kidney Calculi (Kidney Stone)
5. Hydronephrosis

Experts

1. Bajpai, Minu: 2 articles (07/2019 - 10/2014)
2. Goel, Prabudh: 2 articles (07/2019 - 11/2018)
3. Tripathi, Madhavi: 2 articles (07/2019 - 09/2005)
4. Kumar, Santosh: 2 articles (02/2019 - 01/2014)
5. Ansari, M S: 1 article (08/2021)
6. Arya, Amitabh: 1 article (08/2021)
7. Jena, Rahul: 1 article (08/2021)
8. Lal, Hira: 1 article (08/2021)
9. Madhavan, Kumar: 1 article (08/2021)
10. Yadav, Priyank: 1 article (08/2021)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to bilateral Multicystic renal dysplasia:
1. DiureticsIBA
2. TransferasesIBA
3. IsotopesIBA
4. Hexosaminidases (Hexosaminidase)IBA
5. EnzymesIBA
6. Alkaline PhosphataseIBA
7. Furosemide (Lasix)FDA LinkGeneric
8. Radioisotopes (Radionuclides)IBA
9. Epidermal Growth Factor (EGF)IBA
10. Pentetic Acid (DTPA)FDA LinkGeneric

Therapies and Procedures

1. Stents
2. Therapeutics
3. Gamma Cameras (Gamma Camera)
4. Cystectomy
5. Prostatectomy (Retropubic Prostatectomy)