Foix Chavany Marie syndrome

A rare cortico-subcortical suprabulbar or PSEUDOBULBAR PALSY of the lower cranial nerves. It is characterized by severe dysarthria and dysphagia due to paralysis of voluntary movements of the face, tongue, pharynx, and jaw; however, involuntary movements of the affected muscles are preserved.

Also Known As:

Anterior Opercular Syndrome; Bilateral Anterior Opercular Syndrome; Congenital Foix-Chavany-Marie syndrome; Facio-Labio-Pharyngo-Glosso-Laryngo-Brachial Paralysis; Facio-Pharyngo-Glossal Diplegia with Automatic-Voluntary Movement Dissociation; Opercular Syndrome, Anterior; Pseudobulbar Paralysis, Cortical Type

Networked: 1 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Related Diseases

1.	Frontotemporal Lobar Degeneration (Degeneration, Frontotemporal Lobar)
2.	Sialorrhea
3.	Deglutition Disorders (Dysphagia)
4.	Dropped Head Syndrome

Experts

1.	Matej, R: 1 article (06/2007)
2.	Rektorova, I: 1 article (06/2007)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Foix Chavany Marie syndrome:

UbiquitinIBA

06/01/2007 - "Anterior opercular syndrome in frontotemporal lobar degeneration with ubiquitin-only immunoreactive neuronal changes."
06/01/2007 - "This paper presents for the first time an anterior opercular syndrome in association with a gait disorder, dropped head syndrome, dysphagia, and sialorrhea in a neuropathologically proven case of frontotemporal lobar degeneration with ubiquitin inclusions."