Cerebral Amyloidosis with Spongiform Encephalopathy

Cerebellar ataxia, progressive dementia, and amyloid deposits in the central nervous system

Also Known As:

Amyloidosis, Cerebral, with Spongiform Encephalopathy; Cerebellar Ataxia, Progressive Dementia, and Amyloid Deposits In CNS; Prion Dementia

Networked: 5 relevant articles (0 outcomes, 0 trials/studies)

1.	Vascular Dementia (Subcortical Arteriosclerotic Encephalopathy)
2.	Dementia (Dementias)
3.	Brain Diseases (Brain Disorder)
4.	Amyloidosis
5.	Sporadic Creutzfeldt-Jakob Disease

Drugs and Important Biological Agents (IBA) related to Cerebral Amyloidosis with Spongiform Encephalopathy:

1.	Prion ProteinsIBA 01/04/2005 - "Transgenic Tg(PG14) mice express a mutant prion protein containing 14 octapeptide repeats, whose human homologue is associated with an inherited prion dementia. " 05/09/2000 - "We have generated lines of transgenic mice that express a mutant prion protein (PrP) containing 14 octapeptide repeats whose human homologue is associated with an inherited prion dementia. " 01/01/2000 - "We have generated lines of transgenic mice that express a mutant prion protein containing 14 octapeptide repeats whose human homologue is associated with an inherited prion dementia. " 01/16/1993 - "The term "prion dementia" has been proposed to replace "spongiform encephalopathy", to accommodate the existence of atypical forms of these "prion protein" (PrP) cerebral amyloidoses that may not show spongiform changes in the brain. "
2.	PrionsIBA 01/01/2018 - "Patients were divided into three groups: (1) Reversible (treatable) secondary dementia group, (2) Prion dementia group (sporadic Creutzfeldt-Jakob disease), (3) Non-prion Neurodegenerative and vascular dementias (primary neurodegenerative and vascular dementia). "