Hunt's syndrome

Two syndromes with terms bearing Ramsey Hunt: Myoclonic Cerebellar Dyssynergia and Herpes Zoster Oticus

Also Known As:

Myoclonus and Ataxia; Ramsay Hunt Syndrome type 2

Networked: 17 relevant articles (1 outcomes, 2 trials/studies)

Relationship Network

Disease Context: Research Results

Related Diseases

1.	Bell Palsy (Bell's Palsy)
2.	Facial Paralysis (Facial Palsy)
3.	Brain Diseases (Brain Disorder)
4.	Hashimoto Disease (Thyroiditis, Hashimoto)
5.	Mitochondrial Diseases (Mitochondrial Disease)

Experts

1.	Chen, Doujia: 1 article (03/2021)
2.	Chen, Ya: 1 article (03/2021)
3.	Liao, Shusheng: 1 article (03/2021)
4.	Xu, Ping: 1 article (03/2021)
5.	Xu, Zucai: 1 article (03/2021)
6.	Zhang, Haiqing: 1 article (03/2021)
7.	Zhou, Xuejiao: 1 article (03/2021)
8.	Ma, Kam Hung: 1 article (01/2020)
9.	Mak, Chloe M: 1 article (01/2020)
10.	Ng, Grace S F: 1 article (01/2020)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Hunt's syndrome:

1.	Acyclovir (Aciclovir)FDA LinkGeneric 03/01/1992 - "There was a significant reduction of sequelae in patients treated with acyclovir in the group of Ramsay Hunt's syndrome (n = 15) (p less than 0.05). " 03/01/1992 - "In a randomised study, steroids or steroids + acyclovir (oral doses for Bell's palsy, and intravenous doses for Ramsay Hunt's syndrome) were given to 45 patients with facial palsy. "
2.	SteroidsIBA 12/01/2012 - "We describe a unique phenotype: acute onset of myoclonus and ataxia, associated with abnormal opsoclonus-like eye movements; improvement of clinical symptoms under steroid treatment; and appearance of epileptic activity on EEG 2 years later without overt seizures. " 03/01/2023 - "Hypothyroidism-associated hyperkinetic disorders mainly occur in the context of steroid-responsive encephalopathy with autoimmune thyroiditis, that is, Hashimoto disease, mostly manifesting with tremor, myoclonus, and ataxia present in 28-80%, 42-65% and 33-65% in larger series. " 03/01/1992 - "In a randomised study, steroids or steroids + acyclovir (oral doses for Bell's palsy, and intravenous doses for Ramsay Hunt's syndrome) were given to 45 patients with facial palsy. "
3.	dimemorfan (AT 17)IBA 01/01/1988 - "The subjects of the study were 91 patients with Hunt's syndrome and 396 patients with Bell's palsy treated at 17 institutions all over Japan in the period between April 1985 and November 1986. "
4.	Cystatin BIBA 01/01/2023 - "The involvement of mitochondrial dysfunction in cystatin B (CSTB) deficiency has been suggested, but its role in the onset of neurodegeneration, myoclonus, and ataxia in the CSTB-deficient mouse model (Cstb-/-) is yet unknown. "
5.	Proteins (Proteins, Gene)FDA Link 01/01/1989 - "The CSF protein in Hunt's syndrome rose, but its progress was different from that in vestibular neuronitis. "
6.	PrionsIBA 05/01/2007 - "Creutzfeldt-Jakob disease is a prion related disease, characterized by rapidly progressive dementia, associated with myoclonus and ataxia. "
7.	Niacin (Nicotinic Acid)FDA LinkGeneric 02/01/2006 - "In conclusion, we would like to emphasize that administration of niacin should be started for the treatment of chronic alcoholic patients showing myoclonus and ataxia even without the classical triads found in endemic pellagra patients." 02/01/2006 - "[A suspected case of alcoholic pellagra encephalopathy with marked response to niacin showing myoclonus and ataxia as chief complaints]."
8.	MercuryIBA 10/15/2007 - "A 23-year woman, 2 years after injecting herself with elemental mercury developed disabling generalized myoclonus and ataxia. "
9.	Immunoglobulin G (IgG)IBA 01/01/1989 - "In cases of Hunt's syndrome with CSF pleocytosis, intrathecal IgG synthesis was detected. "
10.	Hormones (Hormone)IBA 03/01/2021 - "The patient was treated with hormones and clonazepam, and the symptoms of myoclonus and ataxia disappeared.Results"

Therapies and Procedures

1.	Decompression 01/01/1988 - "To evaluate the benefit of facial nerve decompression for Bell's palsy and Hunt's syndrome, prognoses of patients who underwent surgery were compared with those of patients treated conservatively. " 01/01/1994 - "According to the House grading system for reporting recovery of the facial nerve, in incomplete lesions (Bell's palsy, Hunt's syndrome, trauma etc) treated with nerve total or subtotal decompression (101 cases), transection group produced better voluntary functional movement (average grade 1.66 +/- 0.74) than untransection group (average grade 2.81 +/- 0.87). "
2.	Denervation 01/01/1988 - "The incidence of denervation, as determined electrodiagnostically (nerve excitability test and electroneuronography), was analysed during the course of the disease in 150 patients with Bell's palsy and 45 with Ramsay-Hunt's syndrome. "