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3 Primary ciliary dyskinesia

Also Known As:

Primary ciliary dyskinesia, 3; Ciliary Dyskinesia, Primary, 3; Ciliary Dyskinesia, Primary, 3, with or without Situs Inversus

Networked: 2 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Respiratory Tract Diseases: 6015
Otorhinolaryngologic Diseases: 203
- Ciliary Motility Disorders: 433
  - Kartagener Syndrome: 129
    - 3 Primary ciliary dyskinesia: 2
Cardiovascular Diseases: 91362
- Heart Diseases: 26014
  - Congenital Heart Defects: 8917
    - Dextrocardia: 289
      - Kartagener Syndrome: 129
        3 Primary ciliary dyskinesia: 2
- Cardiovascular Abnormalities: 452
  - Congenital Heart Defects: 8917
    - Dextrocardia: 289
      - Kartagener Syndrome: 129
        3 Primary ciliary dyskinesia: 2
Congenital, Hereditary, and Neonatal Diseases and Abnormalities: 933
- Congenital Abnormalities: 25723
- Inborn Genetic Diseases: 11939
  - Ciliopathies: 604
    - Ciliary Motility Disorders: 433
      - Kartagener Syndrome: 129
        3 Primary ciliary dyskinesia: 2
  - Kartagener Syndrome: 129
    - 3 Primary ciliary dyskinesia: 2

Related Diseases

1.	Infections
2.	Bronchiectasis
3.	Pulmonary Aspergillosis
4.	Inborn Genetic Diseases (Disease, Hereditary)
5.	Sjogren's Syndrome (Sjogren Syndrome)

Experts

1.	Burgel, P-R: 1 article (10/2018)
2.	Chassagnon, G: 1 article (10/2018)
3.	Martin, C: 1 article (10/2018)
4.	Regard, L: 1 article (10/2018)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to 3 Primary ciliary dyskinesia:

1.	Technetium Tc 99m Aggregated AlbuminIBA 03/01/1991 - "We investigated TBC in patients with chronic bronchial infections (bronchiectasis; 11 cases, diffuse panbronchiolitis; 9 cases and primary ciliary dyskinesia; 3 cases) and also in 6 healthy subjects by a radioactive aerosol (99mTc-human serum albumin, 4.4 +/- 1.4 microns in diameter) inhalation scintigraphy with cough control in order to elucidate the relationships between impaired TBC and chronic bronchial infections. "
2.	AerosolsIBA 03/01/1991 - "We investigated TBC in patients with chronic bronchial infections (bronchiectasis; 11 cases, diffuse panbronchiolitis; 9 cases and primary ciliary dyskinesia; 3 cases) and also in 6 healthy subjects by a radioactive aerosol (99mTc-human serum albumin, 4.4 +/- 1.4 microns in diameter) inhalation scintigraphy with cough control in order to elucidate the relationships between impaired TBC and chronic bronchial infections. "

Therapies and Procedures

1.

10/01/2018 - "Main causes of diffuse bronchiectasis can be grouped into 5 categories: (1) immune deficiencies; (2) genetic disorders responsible for abnormal mucociliairy clearance (e.g., cystic fibrosis and primary ciliary dyskinesia); (3) autoinflammatory and connective tissue diseases (e.g., rheumatoid arthritis, Sjogren syndrome); (4) chronic airway inflammatory disorders (e.g., allergic broncho-pulmonary aspergillosis) or chronic infections (e.g., by nontuberculous mycobacteria) and; (5) sequelae of pulmonary insults (e.g., infection, radiotherapy). "