4a- hydroxy- erythro- 5,6,7,8- tetrahydrobiopterin dehydratase
converts (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin to quinoid dihydropterin; defect in Hermansky-Pudlak syndromeresults in decreased levels of biopterin
Also Known As:
4a-OH-6BH4-dehydratase; 4a-hydroxy-6BH4-dehydratase
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Bio-Agent Context: Research Results