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idonic acid (L-idonate)
RN refers to L-idonate
Also Known As:
L-idonate
; L-idonic acid
Networked:
3
relevant articles (
0
outcomes,
0
trials/studies)
Bio-Agent Context: Research Results
Organic Chemicals: 133
Carboxylic Acids: 973
Hydroxy Acids: 94
Sugar Acids: 4
idonic acid: 3
Acyclic Acids
Sugar Acids: 4
idonic acid: 3
Carbohydrates: 22023
Sugar Acids: 4
idonic acid: 3
Experts
1.
Huang, H
: 1 article (04/2020)
2.
Liu, Y P
: 1 article (04/2020)
3.
Wu, X X
: 1 article (04/2020)
4.
Zhang, C F
: 1 article (04/2020)
5.
Zhang, X S
: 1 article (04/2020)
Related Diseases
1.
Mucopolysaccharidosis III (Sanfilippo Syndrome)
12/01/1981 - "
1. Sulphamidase activity was assayed by incubation of the radiolabelled disaccharide O-(alpha-2-sulphamino-2-deoxy-D-glucopyranosyl)- (1 leads to 3)-L-[6-3H]idonic acid with homogenates of leucocytes and cultured skin fibroblasts and concentrates of urine derived from normal individuals, patients affected with sulphamidase deficiency disorder [mucopolysaccharidosis type IIIA (MPS IIIA): the Sanfilippo A syndrome], parents of such patients and patients affected with other mucopolysaccharidoses and lysosomal enzyme deficiencies.
"
02/01/1989 - "
N-Acetylglucosamine-6-sulfatase activity was assayed by incubation of the radiolabeled disaccharide O-(a-N-acetylglucosamine-6-sulfate)-(1----3)-L-[6-3H]-idonic acid (GlcNAc6S-IdOA), with homogenates of leucocytes, cultured fibroblasts, and urine from normal individuals, patients affected with N-acetylglucosamine-6-sulfatase-deficiency (Sanfilippo D syndrome, mucopolysaccharidosis type IIID), and patients affected with other mucopolysaccharidoses and lysosomal storage disorders.
"
2.
Mucopolysaccharidoses
12/01/1981 - "
1. Sulphamidase activity was assayed by incubation of the radiolabelled disaccharide O-(alpha-2-sulphamino-2-deoxy-D-glucopyranosyl)- (1 leads to 3)-L-[6-3H]idonic acid with homogenates of leucocytes and cultured skin fibroblasts and concentrates of urine derived from normal individuals, patients affected with sulphamidase deficiency disorder [mucopolysaccharidosis type IIIA (MPS IIIA): the Sanfilippo A syndrome], parents of such patients and patients affected with other mucopolysaccharidoses and lysosomal enzyme deficiencies.
"
02/01/1989 - "
N-Acetylglucosamine-6-sulfatase activity was assayed by incubation of the radiolabeled disaccharide O-(a-N-acetylglucosamine-6-sulfate)-(1----3)-L-[6-3H]-idonic acid (GlcNAc6S-IdOA), with homogenates of leucocytes, cultured fibroblasts, and urine from normal individuals, patients affected with N-acetylglucosamine-6-sulfatase-deficiency (Sanfilippo D syndrome, mucopolysaccharidosis type IIID), and patients affected with other mucopolysaccharidoses and lysosomal storage disorders.
"
3.
Dehydration (Water Stress)
04/01/2020 - "
Two associated metabolic pathways were identified: L-idonic acid dehydrogenase was found to be involved in the degradation of L-idonic acid through oxidation/decarboxylation in Agrobacterium radiobacter K84, while 2-hydroxy-3-oxopantoate reductase was found to participate in D-glucarate catabolism through dehydration/cleavage in Ralstonia metallidurans CH34.
"
Related Drugs and Biologics
1.
Disaccharides
2.
Sulfates (Sulfates, Inorganic)
3.
Oxidoreductases (Dehydrogenase)
4.
Enzymes
5.
Acetylglucosamine
6.
N-sulfoglucosamine sulfohydrolase (sulfamidase)
7.
N-acetylglucosamine-6-sulfatase