|1.||Arias-Castro, C: 1 article (12/2001)|
|2.||Peraza-Luna, F: 1 article (12/2001)|
|3.||Calva-Calva, G: 1 article (12/2001)|
|4.||Bessiere, J M: 1 article (12/2001)|
|5.||Rodríguez-Mendiola, M: 1 article (12/2001)|
|6.||Korman, S H: 1 article (08/2001)|
|7.||Preminger, A: 1 article (08/2001)|
|8.||Cohen, E: 1 article (08/2001)|
|1.||Maple Syrup Urine Disease
08/01/2001 - "Fenugreek, maple syrup and the urine of maple syrup urine disease (MSUD) patients all share a characteristic odour originating from a common component, sotolone. "
04/01/1999 - "We have shown that sotolone is responsible for the characteristic odour of maple syrup urine disease and, since maple syrup also contains sotolone, the naming of this disease appears to be correct."
04/01/1999 - "Using enantioselective multidimensional gas chromatography-mass spectrometry (enantio-MDGC-MS), we could demonstrate that 4,5-dimethyl-3-hydroxy-2[5H]-furanone (sotolone), a well-known flavour impact compound present in fenugreek and lovage, was present in urine from seven patients with maple syrup urine disease. "
04/01/1999 - "4,5-dimethyl-3-hydroxy-2[5H]-furanone (sotolone)--the odour of maple syrup urine disease."
12/01/2001 - "3-Hydroxy-4,5-dimethyl-2(5H)-furanone (sotolone) and 3-amino-4,5-dimethyl-2(5H)-furanone, the postulated precursor of sotolone, were detected in hairy root cultures of Trigonella foenum-graecum (fenugreek) by GC-MS. The hairy root cultures in both conical flasks and airlift with mesh bioreactors were achieved from hypocotyl of seedling by infection with Agrobacterium rhizogenes. "