|1.||Tuchman, Mendel: 3 articles (10/2011 - 08/2008)|
|2.||Daikhin, Yevgeny: 3 articles (10/2011 - 08/2008)|
|3.||Yudkoff, Marc: 3 articles (10/2011 - 08/2008)|
|4.||Caldovic, Ljubica: 2 articles (10/2011 - 08/2008)|
|5.||Ah Mew, Nicholas: 2 articles (10/2011 - 07/2010)|
|6.||Nissim, Itzhak: 2 articles (07/2010 - 08/2008)|
|7.||Tummolo, Albina: 1 article (05/2013)|
|8.||De Palo, Tommaso: 1 article (05/2013)|
|9.||Bellantuono, Rosa: 1 article (05/2013)|
|10.||Ranieri, Antonio: 1 article (05/2013)|
12/01/2002 - "A therapeutic trial with carbamylglutamate is recommended whenever hyperammonemia without an organic aciduria, increased orotate excretion, or diagnostic amino acidemia/uria is detected."
10/01/2011 - "A 17-year-old female with recurrent hyperammonemia attacks, the cause of which remained undiagnosed for 8 years in spite of multiple molecular and biochemical investigations, showed markedly enhanced ureagenesis (measured by isotope incorporation) in response to N-carbamylglutamate (NCG). "
01/01/2010 - "N-carbamylglutamate in emergency management of hyperammonemia in neonatal acute onset propionic and methylmalonic aciduria."
03/01/1992 - "Treatment of hyperammonemia with carbamylglutamate in rats."
03/01/1992 - "These results indicate that carbamylglutamate, which is not toxic, could be useful in the treatment of hyperammonemia, especially in cirrhosis."
01/01/2012 - "Short-term outcome of propionic aciduria treated at presentation with N-carbamylglutamate: a retrospective review of four patients."
01/01/2005 - "N-carbamylglutamate protects patients with decompensated propionic aciduria from hyperammonaemia."
04/01/2010 - "The aim of this research letter was to describe the use of N-carbamoyl-L-glutamate as first-line treatment of hyperammonemia in a 4-month-old female patient with propionic acidemia (PA). "
04/01/2010 - "Outpatient treatment of propionic acidemia-associated hyperammonemia with N-carbamoyl-L-glutamate in an infant."
01/01/2012 - "N-carbamylglutamate (NCG) has been reported to decrease ammonia levels in patients with propionic aciduria (PA) and methylmalonic aciduria (MMA), but reports on clinical outcomes remain scant. "
|4.||Liver Diseases (Liver Disease)
07/20/1998 - "The findings provide a rational basis for the clinical use of N-carbamoyl-L-glutamate plus L-arginine in the prevention and treatment of hyperammonemia encountered in liver diseases."
12/01/1972 - "The findings reported provide a rational basis for the use of N-carbamoyl-L-glutamate plus L-arginine in the prevention and treatment of hyperammonemia in clinical conditions of liver disease and parental infusion of amino acids, and in feeding of urea supplements to ruminants."
|5.||Inborn Urea Cycle Disorders
|1.||Staphylococcal Protein A (A, Protein)
|7.||Amino-Acid N-Acetyltransferase (N-Acetylglutamate Synthase)
|9.||Biological Markers (Surrogate Marker)