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J S Beckmann Selected Research

Limb-Girdle Muscular Dystrophies (Limb-Girdle Muscular Dystrophy)

06/2001Mutations in calpain 3 associated with limb girdle muscular dystrophy: analysis by molecular modeling and by mutation in m-calpain.
06/2001Pathophysiology of limb girdle muscular dystrophy type 2A: hypothesis and new insights into the IkappaBalpha/NF-kappaB survival pathway in skeletal muscle.
12/2000Secondary reduction in calpain 3 expression in patients with limb girdle muscular dystrophy type 2B and Miyoshi myopathy (primary dysferlinopathies).

Articles by Research Topic

Disease

3Limb-Girdle Muscular Dystrophies (Limb-Girdle Muscular Dystrophy)
06/2001 - 12/2000
2Muscular Diseases (Myopathy)
09/2001 - 12/2000
2Muscular Dystrophies (Muscular Dystrophy)
04/2001 - 12/2000
1Neuromuscular Diseases (Neuromuscular Disease)
08/2002

Drug/Important Bio-Agent (IBA)

3CalpainIBA
06/2001 - 12/2000
2NF-kappaB inhibitor alphaIBA
06/2001 - 12/2000
1Proteins (Proteins, Gene)IBA
08/2002
1N-acylmannosamine kinaseIBA
09/2001
1AcetylglucosamineIBA
09/2001
1Uridine Diphosphate (UDP)IBA
09/2001
1NF-kappa B (NF-kB)IBA
06/2001
1m-calpainIBA
06/2001
1connectin (titin)IBA
04/2001