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Multiple Acyl Coenzyme A Dehydrogenase Deficiency Summary

80 relevant articles (3 outcomes, 4 trials/studies) found for this Disease

Description: An autosomal recessive disorder of fatty acid oxidation, and branched chain amino acids (AMINO ACIDS, BRANCHED-CHAIN); LYSINE; and CHOLINE catabolism, that is due to defects in either subunit of ELECTRON TRANSFER FLAVOPROTEIN or its dehydrogenase, electron transfer flavoprotein-ubiquinone oxidoreductase (EC 1.5.5.1).

Also Known As: ETFA Deficiency; ETFB Deficiency; ETFDH Deficiency; Electron Transfer Flavoprotein Alpha Subunit Deficiency; Electron Transfer Flavoprotein Beta Subunit Deficiency Show All >>

Key Drugs and Agents for Multiple Acyl Coenzyme A Dehydrogenase Deficiency

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Drugs and Important Biological Agents (IBA) related to treatments:
  1. Riboflavin (Vitamin B2) : 1 outcome in 17 results : FDA 8
  2. Carnitine (L-Carnitine) : 1 outcome in 13 results : FDA 9 Generic
  3. Mitochondrial Proteins (Mitochondrial Protein) : 1 outcome in 1 result : IBA
  4. Glycine (Aminoacetic Acid) : 1 outcome in 1 result : FDA 30 Generic
  5. CAV protocol (CHO) : 1 outcome in 1 result : FDA 1
  6. Acyl Coenzyme A (Acyl CoA) : 1 study in 16 results : IBA
  7. Electron-Transferring Flavoproteins (Electron Transfer Flavoprotein) : 1 study in 11 results : IBA
  8. electron-transferring-flavoprotein dehydrogenase (ETF dehydrogenase) : 1 study in 6 results : IBA
  9. Acyl-CoA Dehydrogenases : 1 study in 4 results : IBA
  10. Sarcosine (Methylglycine) : 1 study in 3 results : IBA
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Diseases Related to Multiple Acyl Coenzyme A Dehydrogenase Deficiency

  1. Muscle Weakness
  2. Multiple Acyl Coenzyme A Dehydrogenase Deficiency
  3. Muscular Diseases (Myopathy)
  4. Multiple Carboxylase Deficiency (Deficiency, Multiple Carboxylase)
  5. Polycystic Kidney Diseases (Polycystic Kidney Disease)
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Key Therapies for Multiple Acyl Coenzyme A Dehydrogenase Deficiency

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