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Aggressive Fibromatosis (Desmoid) Summary

461 relevant articles (29 outcomes, 41 trials/studies) found for this Disease

Description: A childhood counterpart of abdominal or extra-abdominal desmoid tumors, characterized by firm subcutaneous nodules that grow rapidly in any part of the body but do not metastasize. The adult form of abdominal fibromatosis is FIBROMATOSIS, ABDOMINAL. (Stedman, 25th ed)

Also Known As: Desmoid; Fibromatosis, Aggressive; Aggressive Fibromatoses; Desmoids; Fibromatoses, Aggressive

Key Drugs and Agents for Aggressive Fibromatosis

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Drugs and Important Biological Agents (IBA) related to treatments:
  1. Tamoxifen : 9 outcomes 3 studies in 44 results : FDA 12 Generic
  2. Sulindac (Copal) : 3 outcomes 1 study in 19 results : FDA 15 Generic
  3. Toremifene (Fareston) : 2 outcomes 1 study in 12 results : FDA 1
  4. Estrogens (Estrogen) : 2 outcomes in 16 results : FDA 1
  5. Interferons : 2 outcomes in 3 results : IBA
  6. imatinib (Gleevec) : 1 outcome 4 studies in 9 results : FDA 2
  7. Estrogen Receptor Modulators (Antiestrogen) : 1 outcome 1 study in 9 results : IBA
  8. Raloxifene (Evista) : 1 outcome 1 study in 3 results : FDA 2
  9. pirfenidone : 1 outcome 1 study in 1 result : IBA
  10. Doxorubicin (Adriamycin) : 1 outcome in 8 results : FDA 12 Generic
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Diseases Related to Aggressive Fibromatosis

  1. Neoplasms (Cancer)
  2. Retroperitoneal Fibrosis
  3. Adenomatous Polyposis Coli (Familial Adenomatous Polyposis)
  4. Sarcoma (Soft Tissue Sarcoma)
  5. Fibroma (Fibromatosis)
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Key Therapies for Aggressive Fibromatosis

Efficacy Chart >>
  1. Drug Therapy (Chemotherapy) : 6 outcomes 2 studies in 39 results
  2. Colectomy : 2 outcomes 1 study in 34 results
  3. Brachytherapy : 1 outcome in 5 results
  4. Limb Salvage : 1 outcome in 2 results
  5. Neoadjuvant Therapy : 1 outcome in 2 results
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